Loss of p53 causes mitochondrial DNA depletion and altered mitochondrial reactive oxygen species homeostasis

In addition to its central role in cellular stress signaling, the tumor suppressor p53 modulates mitochondrial respiration through its nuclear transcription factor activity and localizes to mitochondria, where it enhances apoptosis and suppresses mitochondrial DNA (mtDNA) mutagenesis. Here we demons...

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Vydané v:Biochimica et biophysica acta Ročník 1787; číslo 5; s. 328 - 334
Hlavní autori: Lebedeva, Maria A., Eaton, Jana S., Shadel, Gerald S.
Médium: Journal Article
Jazyk:English
Vydavateľské údaje: Netherlands Elsevier B.V 01.05.2009
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ISSN:0005-2728, 0006-3002, 1879-2650
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Abstract In addition to its central role in cellular stress signaling, the tumor suppressor p53 modulates mitochondrial respiration through its nuclear transcription factor activity and localizes to mitochondria, where it enhances apoptosis and suppresses mitochondrial DNA (mtDNA) mutagenesis. Here we demonstrate a new conserved role for p53 in mtDNA copy number maintenance and mitochondrial reactive oxygen species (ROS) homeostasis. In mammals, mtDNA is present at thousands of copies per cell and is essential for normal development and cell function. We show that p53 null mouse and p53 knockdown human primary fibroblasts exhibit mtDNA depletion and decreased mitochondrial mass under normal culture growth conditions. This is accompanied by a reduction of the p53R2 subunit of ribonucleotide reductase mRNA and protein and of mitochondrial transcription factor A (mtTFA) at the protein level only. Finally, p53-depleted cells exhibit significant disruption of cellular ROS homeostasis, characterized by reduced mitochondrial and cellular superoxide levels and increased cellular hydrogen peroxide. Altogether, these results elucidate additional mitochondria-related functions for p53 and implicate mtDNA depletion and ROS alterations as potentially relevant to cellular transformation, cancer cell phenotypes, and the Warburg Effect.
AbstractList In addition to its central role in cellular stress signaling, the tumor suppressor p53 modulates mitochondrial respiration through its nuclear transcription factor activity and localizes to mitochondria, where it enhances apoptosis and suppresses mitochondrial DNA (mtDNA) mutagenesis. Here we demonstrate a new conserved role for p53 in mtDNA copy number maintenance and mitochondrial reactive oxygen species (ROS) homeostasis. In mammals, mtDNA is present at thousands of copies per cell and is essential for normal development and cell function. We show that p53 null mouse and p53 knockdown human primary fibroblasts exhibit mtDNA depletion and decreased mitochondrial mass under normal culture growth conditions. This is accompanied by a reduction of the p53R2 subunit of ribonucleotide reductase mRNA and protein and of mitochondrial transcription factor A (mtTFA) at the protein level only. Finally, p53-depleted cells exhibit significant disruption of cellular ROS homeostasis, characterized by reduced mitochondrial and cellular superoxide levels and increased cellular hydrogen peroxide. Altogether, these results elucidate additional mitochondria-related functions for p53 and implicate mtDNA depletion and ROS alterations as potentially relevant to cellular transformation, cancer cell phenotypes, and the Warburg Effect.
Author Eaton, Jana S.
Lebedeva, Maria A.
Shadel, Gerald S.
Author_xml – sequence: 1
  givenname: Maria A.
  surname: Lebedeva
  fullname: Lebedeva, Maria A.
  organization: Department of Pathology, Yale University School of Medicine, 310 Cedar Street, P.O. Box 208023, New Haven, CT 06520-8023, USA
– sequence: 2
  givenname: Jana S.
  surname: Eaton
  fullname: Eaton, Jana S.
  organization: Department of Pathology, Yale University School of Medicine, 310 Cedar Street, P.O. Box 208023, New Haven, CT 06520-8023, USA
– sequence: 3
  givenname: Gerald S.
  surname: Shadel
  fullname: Shadel, Gerald S.
  email: gerald.shadel@yale.edu
  organization: Department of Pathology, Yale University School of Medicine, 310 Cedar Street, P.O. Box 208023, New Haven, CT 06520-8023, USA
BackLink https://www.ncbi.nlm.nih.gov/pubmed/19413947$$D View this record in MEDLINE/PubMed
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Cites_doi 10.1007/s10863-007-9083-0
10.1074/jbc.M512894200
10.1016/S0955-0674(03)00002-4
10.1016/j.cell.2006.05.036
10.1038/ng2040
10.1038/sj.onc.1203774
10.1038/sj.onc.1204101
10.1002/1522-2683(20001001)21:16<3427::AID-ELPS3427>3.0.CO;2-L
10.1038/35003506
10.1016/j.molcel.2006.11.024
10.1038/sj.emboj.7600819
10.1016/j.febslet.2004.10.099
10.1016/0167-4838(96)00089-1
10.1016/j.cell.2008.06.016
10.1016/S1097-2765(04)00179-0
10.1152/physrev.00025.2007
10.1016/j.mito.2004.05.010
10.1042/0264-6021:3540243
10.1111/j.1474-9726.2008.00411.x
10.1038/sj.emboj.7601560
10.1126/science.1126863
10.4161/cc.6.16.4572
10.1093/hmg/3.10.1763
10.2353/ajpath.2008.071163
10.1172/JCI31604
10.1091/mbc.E05-01-0053
10.1126/science.1092734
10.1038/ng0398-231
10.1146/annurev.med.59.053006.104646
10.1128/MCB.24.15.6728-6741.2004
10.1158/0008-5472.CAN-05-4103
10.1158/0008-5472.CAN-2287-2
10.1146/annurev.genet.39.110304.095751
10.1093/nar/gkm635
10.1074/jbc.M701310200
10.1113/jphysiol.2003.049478
10.1158/0008-5472.CAN-04-3835
10.1089/dna.2004.23.797
10.1016/j.gene.2005.03.031
10.1096/fj.00-0262com
10.1093/hmg/ddn280
10.1093/nar/30.9.1929
10.1016/j.tcb.2007.04.004
10.1126/science.124.3215.269
10.1186/1476-4598-7-54
10.1074/jbc.275.21.16202
10.1038/nm1320
10.1007/s00109-002-0343-5
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Keywords Mitochondrial transcription factor A
Reactive oxygen species
mtDNA depletion
p53R2
p53
Cancer
Language English
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References Hakansson, Hofer, Thelander (bib18) 2006; 281
Nakano, Balint, Ashcroft, Vousden (bib34) 2000; 19
Larsson, Wang, Wilhelmsson, Oldfors, Rustin, Lewandoski, Barsh, Clayton (bib35) 1998; 18
Butow, Avadhani (bib11) 2004; 14
Bensaad, Tsuruta, Selak, Vidal, Nakano, Bartrons, Gottlieb, Vousden (bib45) 2006; 126
Sablina, Budanov, Ilyinskaya, Agapova, Kravchenko, Chumakov (bib44) 2005; 11
Pagliarini, Calvo, Chang, Sheth, Vafai, Ong, Walford, Sugiana, Boneh, Chen, Hill, Vidal, Evans, Thorburn, Carr, Mootha (bib8) 2008; 134
Lebedeva, Shadel (bib17) 2007; 6
Poulton, Morten, Freeman-Emmerson, Potter, Sewry, Dubowitz, Kidd, Stephenson, Whitehouse, Hansen (bib38) 1994; 3
Scarpulla (bib10) 2008; 88
Warburg (bib50) 1956; 124
Chen, Yu, Zhu, Lopez (bib25) 2006; 66
Krishnan, Greaves, Reeve, Turnbull (bib3) 2007; 35
Elpeleg, Mandel, Saada (bib6) 2002; 80
Matoba, Kang, Patino, Wragg, Boehm, Gavrilova, Hurley, Bunz, Hwang (bib32) 2006; 312
Tanaka, Arakawa, Yamaguchi, Shiraishi, Fukuda, Matsui, Takei, Nakamura (bib33) 2000; 404
Erster, Mihara, Kim, Petrenko, Moll (bib23) 2004; 24
Heyne, Schmitt, Mueller, Armbruester, Mestres, Roemer (bib43) 2008; 7
Turrens (bib31) 2003; 552
Yates, Korbel, Shtutman, Roninson, DiMaio (bib29) 2008; 7
Lopez, Kristal, Chernokalskaya, Lazarev, Shestopalov, Bogdanova, Robinson (bib9) 2000; 21
Bensaad, Vousden (bib20) 2007; 17
O'Rourke, Doudican, Zhang, Eaton, Doetsch, Shadel (bib15) 2005; 354
Hussain, Amstad, He, Robles, Lupold, Kaneko, Ichimiya, Sengupta, Mechanic, Okamura, Hofseth, Moake, Nagashima, Forrester, Harris (bib46) 2004; 64
Taylor, Zhang, Eaton, Rodeheffer, Lebedeva, O'Rourke, Siede, Shadel (bib16) 2005; 16
Yoshida, Izumi, Torigoe, Ishiguchi, Itoh, Kang, Kohno (bib28) 2003; 63
Marchenko, Zaika, Moll (bib40) 2000; 275
Shadel (bib1) 2008; 172
Saada (bib13) 2004; 23
Chipuk, Kuwana, Bouchier-Hayes, Droin, Newmeyer, Schuler, Green (bib22) 2004; 303
Hakonen, Goffart, Marjavaara, Paetau, Cooper, Mattila, Lampinen, Sajantila, Lonnqvist, Spelbrink, Suomalainen (bib7) 2008; 17
Merrick, He, Witcher, Patterson, Reid, Pence-Pawlowski, Selkirk (bib39) 1996; 1297
Lewis (bib5) 2004; 4
Ma, Sung, Park, Matoba, Hwang (bib21) 2007; 39
Donahue, Razmara, Hoek, Knudsen (bib27) 2001; 15
Goto, Matsushima, Kadowaki, Kitagawa (bib36) 2001; 354
Marchenko, Wolff, Erster, Becker, Moll (bib41) 2007; 26
Copeland (bib12) 2008; 59
Eaton, Lin, Sartorelli, Bonawitz, Shadel (bib4) 2007; 117
Pontarin, Ferraro, Hakansson, Thelander, Reichard, Bianchi (bib19) 2007; 282
Seidel-Rogol, Shadel (bib37) 2002; 30
Achanta, Sasaki, Feng, Carew, Lu, Pelicano, Keating, Huang (bib24) 2005; 24
Sambrook, Fritsch, Maniatis (bib30) 1989
Bonawitz, Clayton, Shadel (bib42) 2006; 24
Drane, Bravard, Bouvard, May (bib47) 2001; 20
Finkel (bib51) 2003; 15
Wallace (bib2) 2005; 39
Heyne, Mannebach, Wuertz, Knaup, Mahyar-Roemer, Roemer (bib26) 2004; 578
Pani, Bedogni, Anzevino, Colavitti, Palazzotti, Borrello, Galeotti (bib48) 2000; 60
Zhao, Chaiswing, Velez, Batinic-Haberle, Colburn, Oberley, St Clair (bib49) 2005; 65
Bourdon, Minai, Serre, Jais, Sarzi, Aubert, Chretien, de Lonlay, Paquis-Flucklinger, Arakawa, Nakamura, Munnich, Rotig (bib14) 2007; 39
Lopez (10.1016/j.bbabio.2009.01.004_bib9) 2000; 21
Merrick (10.1016/j.bbabio.2009.01.004_bib39) 1996; 1297
Chipuk (10.1016/j.bbabio.2009.01.004_bib22) 2004; 303
Bonawitz (10.1016/j.bbabio.2009.01.004_bib42) 2006; 24
Pani (10.1016/j.bbabio.2009.01.004_bib48) 2000; 60
Pontarin (10.1016/j.bbabio.2009.01.004_bib19) 2007; 282
Heyne (10.1016/j.bbabio.2009.01.004_bib43) 2008; 7
Yoshida (10.1016/j.bbabio.2009.01.004_bib28) 2003; 63
Turrens (10.1016/j.bbabio.2009.01.004_bib31) 2003; 552
Poulton (10.1016/j.bbabio.2009.01.004_bib38) 1994; 3
Sambrook (10.1016/j.bbabio.2009.01.004_bib30) 1989
Scarpulla (10.1016/j.bbabio.2009.01.004_bib10) 2008; 88
Lewis (10.1016/j.bbabio.2009.01.004_bib5) 2004; 4
Marchenko (10.1016/j.bbabio.2009.01.004_bib41) 2007; 26
Zhao (10.1016/j.bbabio.2009.01.004_bib49) 2005; 65
Drane (10.1016/j.bbabio.2009.01.004_bib47) 2001; 20
O'Rourke (10.1016/j.bbabio.2009.01.004_bib15) 2005; 354
Bensaad (10.1016/j.bbabio.2009.01.004_bib20) 2007; 17
Chen (10.1016/j.bbabio.2009.01.004_bib25) 2006; 66
Donahue (10.1016/j.bbabio.2009.01.004_bib27) 2001; 15
Wallace (10.1016/j.bbabio.2009.01.004_bib2) 2005; 39
Saada (10.1016/j.bbabio.2009.01.004_bib13) 2004; 23
Goto (10.1016/j.bbabio.2009.01.004_bib36) 2001; 354
Finkel (10.1016/j.bbabio.2009.01.004_bib51) 2003; 15
Bensaad (10.1016/j.bbabio.2009.01.004_bib45) 2006; 126
Butow (10.1016/j.bbabio.2009.01.004_bib11) 2004; 14
Ma (10.1016/j.bbabio.2009.01.004_bib21) 2007; 39
Lebedeva (10.1016/j.bbabio.2009.01.004_bib17) 2007; 6
Krishnan (10.1016/j.bbabio.2009.01.004_bib3) 2007; 35
Pagliarini (10.1016/j.bbabio.2009.01.004_bib8) 2008; 134
Larsson (10.1016/j.bbabio.2009.01.004_bib35) 1998; 18
Heyne (10.1016/j.bbabio.2009.01.004_bib26) 2004; 578
Seidel-Rogol (10.1016/j.bbabio.2009.01.004_bib37) 2002; 30
Sablina (10.1016/j.bbabio.2009.01.004_bib44) 2005; 11
Warburg (10.1016/j.bbabio.2009.01.004_bib50) 1956; 124
Matoba (10.1016/j.bbabio.2009.01.004_bib32) 2006; 312
Eaton (10.1016/j.bbabio.2009.01.004_bib4) 2007; 117
Bourdon (10.1016/j.bbabio.2009.01.004_bib14) 2007; 39
Achanta (10.1016/j.bbabio.2009.01.004_bib24) 2005; 24
Erster (10.1016/j.bbabio.2009.01.004_bib23) 2004; 24
Tanaka (10.1016/j.bbabio.2009.01.004_bib33) 2000; 404
Marchenko (10.1016/j.bbabio.2009.01.004_bib40) 2000; 275
Shadel (10.1016/j.bbabio.2009.01.004_bib1) 2008; 172
Elpeleg (10.1016/j.bbabio.2009.01.004_bib6) 2002; 80
Copeland (10.1016/j.bbabio.2009.01.004_bib12) 2008; 59
Nakano (10.1016/j.bbabio.2009.01.004_bib34) 2000; 19
Taylor (10.1016/j.bbabio.2009.01.004_bib16) 2005; 16
Hakonen (10.1016/j.bbabio.2009.01.004_bib7) 2008; 17
Yates (10.1016/j.bbabio.2009.01.004_bib29) 2008; 7
Hakansson (10.1016/j.bbabio.2009.01.004_bib18) 2006; 281
Hussain (10.1016/j.bbabio.2009.01.004_bib46) 2004; 64
References_xml – volume: 134
  start-page: 112
  year: 2008
  end-page: 123
  ident: bib8
  article-title: A mitochondrial protein compendium elucidates complex I disease biology
  publication-title: Cell
– volume: 88
  start-page: 611
  year: 2008
  end-page: 638
  ident: bib10
  article-title: Transcriptional paradigms in mammalian mitochondrial biogenesis and function
  publication-title: Physiol. Rev.
– volume: 39
  start-page: 776
  year: 2007
  end-page: 780
  ident: bib14
  article-title: Mutation of RRM2B, encoding p53-controlled ribonucleotide reductase (p53R2), causes severe mitochondrial DNA depletion
  publication-title: Nat. Genet.
– volume: 26
  start-page: 923
  year: 2007
  end-page: 934
  ident: bib41
  article-title: Monoubiquitylation promotes mitochondrial p53 translocation
  publication-title: EMBO J.
– volume: 172
  start-page: 1445
  year: 2008
  end-page: 1456
  ident: bib1
  article-title: Expression and maintenance of mitochondrial DNA: new insights into human disease pathology
  publication-title: Am. J. Pathol.
– volume: 16
  start-page: 3010
  year: 2005
  end-page: 3018
  ident: bib16
  article-title: The conserved Mec1/Rad53 nuclear checkpoint pathway regulates mitochondrial DNA copy number in
  publication-title: Mol. Biol. Cell
– volume: 19
  start-page: 4283
  year: 2000
  end-page: 4289
  ident: bib34
  article-title: A ribonucleotide reductase gene is a transcriptional target of p53 and p73
  publication-title: Oncogene
– volume: 24
  start-page: 6728
  year: 2004
  end-page: 6741
  ident: bib23
  article-title: In vivo mitochondrial p53 translocation triggers a rapid first wave of cell death in response to DNA damage that can precede p53 target gene activation
  publication-title: Mol. Cell. Biol.
– volume: 15
  start-page: 247
  year: 2003
  end-page: 254
  ident: bib51
  article-title: Oxidant signals and oxidative stress
  publication-title: Curr. Opin. Cell Biol.
– volume: 281
  start-page: 7834
  year: 2006
  end-page: 7841
  ident: bib18
  article-title: Regulation of mammalian ribonucleotide reduction and dNTP pools after DNA damage and in resting cells
  publication-title: J. Biol. Chem.
– volume: 303
  start-page: 1010
  year: 2004
  end-page: 1014
  ident: bib22
  article-title: Direct activation of Bax by p53 mediates mitochondrial membrane permeabilization and apoptosis
  publication-title: Science (New York, N.Y
– volume: 80
  start-page: 389
  year: 2002
  end-page: 396
  ident: bib6
  article-title: Depletion of the other genome-mitochondrial DNA depletion syndromes in humans
  publication-title: J. Mol. Med.
– volume: 6
  start-page: 2048
  year: 2007
  end-page: 2057
  ident: bib17
  article-title: Cell cycle- and ribonucleotide reductase-driven changes in mtDNA copy number influence mtDNA Inheritance without compromising mitochondrial gene expression
  publication-title: Cell Cycle (Georgetown, Tex)
– volume: 17
  start-page: 3822
  year: 2008
  end-page: 3835
  ident: bib7
  article-title: Infantile-onset spinocerebellar ataxia and mitochondrial recessive ataxia syndrome are associated with neuronal complex I defect and mtDNA depletion
  publication-title: Hum. Mol. Genet.
– volume: 60
  start-page: 4654
  year: 2000
  end-page: 4660
  ident: bib48
  article-title: Deregulated manganese superoxide dismutase expression and resistance to oxidative injury in p53-deficient cells
  publication-title: Cancer Res.
– volume: 39
  start-page: 243
  year: 2007
  end-page: 246
  ident: bib21
  article-title: A pivotal role for p53: balancing aerobic respiration and glycolysis
  publication-title: J. Bioenerg. Biomembr.
– volume: 354
  start-page: 243
  year: 2001
  end-page: 248
  ident: bib36
  article-title: mitochondrial transcription factor A (d-TFAM) is dispensable for the transcription of mitochondrial DNA in Kc167 cells
  publication-title: Biochem. J.
– volume: 59
  start-page: 131
  year: 2008
  end-page: 146
  ident: bib12
  article-title: Inherited mitochondrial diseases of DNA replication
  publication-title: Annu. Rev. Med.
– volume: 66
  start-page: 3485
  year: 2006
  end-page: 3494
  ident: bib25
  article-title: The p53 pathway promotes efficient mitochondrial DNA base excision repair in colorectal cancer cells
  publication-title: Cancer Res.
– volume: 126
  start-page: 107
  year: 2006
  end-page: 120
  ident: bib45
  article-title: TIGAR, a p53-inducible regulator of glycolysis and apoptosis
  publication-title: Cell
– volume: 404
  start-page: 42
  year: 2000
  end-page: 49
  ident: bib33
  article-title: A ribonucleotide reductase gene involved in a p53-dependent cell-cycle checkpoint for DNA damage
  publication-title: Nature
– volume: 18
  start-page: 231
  year: 1998
  end-page: 236
  ident: bib35
  article-title: Mitochondrial transcription factor A is necessary for mtDNA maintenance and embryogenesis in mice
  publication-title: Nat. Genet.
– volume: 354
  start-page: 86
  year: 2005
  end-page: 92
  ident: bib15
  article-title: Differential involvement of the related DNA helicases Pif1p and Rrm3p in mtDNA point mutagenesis and stability
  publication-title: Gene
– volume: 282
  start-page: 16820
  year: 2007
  end-page: 16828
  ident: bib19
  article-title: p53R2-dependent ribonucleotide reduction provides deoxyribonucleotides in quiescent human fibroblasts in the absence of induced DNA damage
  publication-title: J. Biol. Chem.
– volume: 39
  start-page: 359
  year: 2005
  end-page: 407
  ident: bib2
  article-title: A mitochondrial paradigm of metabolic and degenerative diseases, aging, and cancer: a dawn for evolutionary medicine
  publication-title: Annu. Rev. Genet.
– volume: 578
  start-page: 198
  year: 2004
  end-page: 202
  ident: bib26
  article-title: Identification of a putative p53 binding sequence within the human mitochondrial genome
  publication-title: FEBS Lett.
– volume: 30
  start-page: 1929
  year: 2002
  end-page: 1934
  ident: bib37
  article-title: Modulation of mitochondrial transcription in response to mtDNA depletion and repletion in HeLa cells
  publication-title: Nucleic Acids Res.
– volume: 65
  start-page: 3745
  year: 2005
  end-page: 3750
  ident: bib49
  article-title: p53 translocation to mitochondria precedes its nuclear translocation and targets mitochondrial oxidative defense protein-manganese superoxide dismutase
  publication-title: Cancer Res.
– volume: 312
  start-page: 1650
  year: 2006
  end-page: 1653
  ident: bib32
  article-title: p53 regulates mitochondrial respiration
  publication-title: Science (New York, N.Y
– volume: 4
  start-page: 141
  year: 2004
  end-page: 152
  ident: bib5
  article-title: Cardiomyopathy, nucleoside reverse transcriptase inhibitors and mitochondria are linked through AIDS and its therapy
  publication-title: Mitochondrion
– volume: 3
  start-page: 1763
  year: 1994
  end-page: 1769
  ident: bib38
  article-title: Deficiency of the human mitochondrial transcription factor h-mtTFA in infantile mitochondrial myopathy is associated with mtDNA depletion
  publication-title: Hum. Mol. Genet.
– volume: 552
  start-page: 335
  year: 2003
  end-page: 344
  ident: bib31
  article-title: Mitochondrial formation of reactive oxygen species
  publication-title: J. Physiol.
– volume: 275
  start-page: 16202
  year: 2000
  end-page: 16212
  ident: bib40
  article-title: Death signal-induced localization of p53 protein to mitochondria. A potential role in apoptotic signaling
  publication-title: J. Biol. Chem.
– volume: 11
  start-page: 1306
  year: 2005
  end-page: 1313
  ident: bib44
  article-title: The antioxidant function of the p53 tumor suppressor
  publication-title: Nat. Med.
– volume: 20
  start-page: 430
  year: 2001
  end-page: 439
  ident: bib47
  article-title: Reciprocal down-regulation of p53 and SOD2 gene expression-implication in p53 mediated apoptosis
  publication-title: Oncogene
– volume: 64
  start-page: 2350
  year: 2004
  end-page: 2356
  ident: bib46
  article-title: p53-induced up-regulation of MnSOD and GPx but not catalase increases oxidative stress and apoptosis
  publication-title: Cancer Res.
– volume: 7
  start-page: 54
  year: 2008
  ident: bib43
  article-title: Resistance of mitochondrial p53 to dominant inhibition
  publication-title: Mol. Cancer
– volume: 24
  start-page: 3482
  year: 2005
  end-page: 3492
  ident: bib24
  article-title: Novel role of p53 in maintaining mitochondrial genetic stability through interaction with DNA Pol gamma
  publication-title: EMBO J.
– volume: 124
  start-page: 269
  year: 1956
  end-page: 270
  ident: bib50
  article-title: On respiratory impairment in cancer cells
  publication-title: Science (New York, N.Y
– volume: 15
  start-page: 635
  year: 2001
  end-page: 644
  ident: bib27
  article-title: Direct influence of the p53 tumor suppressor on mitochondrial biogenesis and function
  publication-title: FASEB J.
– volume: 17
  start-page: 286
  year: 2007
  end-page: 291
  ident: bib20
  article-title: p53: new roles in metabolism
  publication-title: Trends Cell Biol.
– volume: 117
  start-page: 2723
  year: 2007
  end-page: 2734
  ident: bib4
  article-title: Ataxia-telangiectasia mutated kinase regulates ribonucleotide reductase and mitochondrial homeostasis
  publication-title: J. Clin. Invest.
– volume: 63
  start-page: 3729
  year: 2003
  end-page: 3734
  ident: bib28
  article-title: P53 physically interacts with mitochondrial transcription factor A and differentially regulates binding to damaged DNA
  publication-title: Cancer Res.
– year: 1989
  ident: bib30
  article-title: Molecular Cloning: A Laboratory Manual
– volume: 35
  start-page: 7399
  year: 2007
  end-page: 7405
  ident: bib3
  article-title: The ageing mitochondrial genome
  publication-title: Nucleic Acids Res.
– volume: 23
  start-page: 797
  year: 2004
  end-page: 806
  ident: bib13
  article-title: Deoxyribonucleotides and disorders of mitochondrial DNA integrity
  publication-title: DNA Cell Biol.
– volume: 7
  start-page: 609
  year: 2008
  end-page: 621
  ident: bib29
  article-title: Repression of the SUMO-specific protease Senp1 induces p53-dependent premature senescence in normal human fibroblasts
  publication-title: Aging cell
– volume: 1297
  start-page: 57
  year: 1996
  end-page: 68
  ident: bib39
  article-title: HSP binding and mitochondrial localization of p53 protein in human HT1080 and mouse C3H10T1/2 cell lines
  publication-title: Biochim. Biophys. Acta
– volume: 21
  start-page: 3427
  year: 2000
  end-page: 3440
  ident: bib9
  article-title: High-throughput profiling of the mitochondrial proteome using affinity fractionation and automation
  publication-title: Electrophoresis
– volume: 14
  start-page: 1
  year: 2004
  end-page: 15
  ident: bib11
  article-title: Mitochondrial signaling: the retrograde response
  publication-title: Mol. Cell
– volume: 24
  start-page: 813
  year: 2006
  end-page: 825
  ident: bib42
  article-title: Initiation and beyond: multiple functions of the human mitochondrial transcription machinery
  publication-title: Mol. Cell
– volume: 39
  start-page: 243
  year: 2007
  ident: 10.1016/j.bbabio.2009.01.004_bib21
  article-title: A pivotal role for p53: balancing aerobic respiration and glycolysis
  publication-title: J. Bioenerg. Biomembr.
  doi: 10.1007/s10863-007-9083-0
– volume: 281
  start-page: 7834
  year: 2006
  ident: 10.1016/j.bbabio.2009.01.004_bib18
  article-title: Regulation of mammalian ribonucleotide reduction and dNTP pools after DNA damage and in resting cells
  publication-title: J. Biol. Chem.
  doi: 10.1074/jbc.M512894200
– volume: 15
  start-page: 247
  year: 2003
  ident: 10.1016/j.bbabio.2009.01.004_bib51
  article-title: Oxidant signals and oxidative stress
  publication-title: Curr. Opin. Cell Biol.
  doi: 10.1016/S0955-0674(03)00002-4
– volume: 126
  start-page: 107
  year: 2006
  ident: 10.1016/j.bbabio.2009.01.004_bib45
  article-title: TIGAR, a p53-inducible regulator of glycolysis and apoptosis
  publication-title: Cell
  doi: 10.1016/j.cell.2006.05.036
– volume: 39
  start-page: 776
  year: 2007
  ident: 10.1016/j.bbabio.2009.01.004_bib14
  article-title: Mutation of RRM2B, encoding p53-controlled ribonucleotide reductase (p53R2), causes severe mitochondrial DNA depletion
  publication-title: Nat. Genet.
  doi: 10.1038/ng2040
– volume: 19
  start-page: 4283
  year: 2000
  ident: 10.1016/j.bbabio.2009.01.004_bib34
  article-title: A ribonucleotide reductase gene is a transcriptional target of p53 and p73
  publication-title: Oncogene
  doi: 10.1038/sj.onc.1203774
– volume: 20
  start-page: 430
  year: 2001
  ident: 10.1016/j.bbabio.2009.01.004_bib47
  article-title: Reciprocal down-regulation of p53 and SOD2 gene expression-implication in p53 mediated apoptosis
  publication-title: Oncogene
  doi: 10.1038/sj.onc.1204101
– volume: 21
  start-page: 3427
  year: 2000
  ident: 10.1016/j.bbabio.2009.01.004_bib9
  article-title: High-throughput profiling of the mitochondrial proteome using affinity fractionation and automation
  publication-title: Electrophoresis
  doi: 10.1002/1522-2683(20001001)21:16<3427::AID-ELPS3427>3.0.CO;2-L
– volume: 404
  start-page: 42
  year: 2000
  ident: 10.1016/j.bbabio.2009.01.004_bib33
  article-title: A ribonucleotide reductase gene involved in a p53-dependent cell-cycle checkpoint for DNA damage
  publication-title: Nature
  doi: 10.1038/35003506
– volume: 24
  start-page: 813
  year: 2006
  ident: 10.1016/j.bbabio.2009.01.004_bib42
  article-title: Initiation and beyond: multiple functions of the human mitochondrial transcription machinery
  publication-title: Mol. Cell
  doi: 10.1016/j.molcel.2006.11.024
– volume: 24
  start-page: 3482
  year: 2005
  ident: 10.1016/j.bbabio.2009.01.004_bib24
  article-title: Novel role of p53 in maintaining mitochondrial genetic stability through interaction with DNA Pol gamma
  publication-title: EMBO J.
  doi: 10.1038/sj.emboj.7600819
– volume: 60
  start-page: 4654
  year: 2000
  ident: 10.1016/j.bbabio.2009.01.004_bib48
  article-title: Deregulated manganese superoxide dismutase expression and resistance to oxidative injury in p53-deficient cells
  publication-title: Cancer Res.
– volume: 578
  start-page: 198
  year: 2004
  ident: 10.1016/j.bbabio.2009.01.004_bib26
  article-title: Identification of a putative p53 binding sequence within the human mitochondrial genome
  publication-title: FEBS Lett.
  doi: 10.1016/j.febslet.2004.10.099
– volume: 1297
  start-page: 57
  year: 1996
  ident: 10.1016/j.bbabio.2009.01.004_bib39
  article-title: HSP binding and mitochondrial localization of p53 protein in human HT1080 and mouse C3H10T1/2 cell lines
  publication-title: Biochim. Biophys. Acta
  doi: 10.1016/0167-4838(96)00089-1
– volume: 134
  start-page: 112
  year: 2008
  ident: 10.1016/j.bbabio.2009.01.004_bib8
  article-title: A mitochondrial protein compendium elucidates complex I disease biology
  publication-title: Cell
  doi: 10.1016/j.cell.2008.06.016
– volume: 14
  start-page: 1
  year: 2004
  ident: 10.1016/j.bbabio.2009.01.004_bib11
  article-title: Mitochondrial signaling: the retrograde response
  publication-title: Mol. Cell
  doi: 10.1016/S1097-2765(04)00179-0
– volume: 88
  start-page: 611
  year: 2008
  ident: 10.1016/j.bbabio.2009.01.004_bib10
  article-title: Transcriptional paradigms in mammalian mitochondrial biogenesis and function
  publication-title: Physiol. Rev.
  doi: 10.1152/physrev.00025.2007
– volume: 4
  start-page: 141
  year: 2004
  ident: 10.1016/j.bbabio.2009.01.004_bib5
  article-title: Cardiomyopathy, nucleoside reverse transcriptase inhibitors and mitochondria are linked through AIDS and its therapy
  publication-title: Mitochondrion
  doi: 10.1016/j.mito.2004.05.010
– volume: 354
  start-page: 243
  year: 2001
  ident: 10.1016/j.bbabio.2009.01.004_bib36
  article-title: Drosophila mitochondrial transcription factor A (d-TFAM) is dispensable for the transcription of mitochondrial DNA in Kc167 cells
  publication-title: Biochem. J.
  doi: 10.1042/0264-6021:3540243
– volume: 7
  start-page: 609
  year: 2008
  ident: 10.1016/j.bbabio.2009.01.004_bib29
  article-title: Repression of the SUMO-specific protease Senp1 induces p53-dependent premature senescence in normal human fibroblasts
  publication-title: Aging cell
  doi: 10.1111/j.1474-9726.2008.00411.x
– volume: 26
  start-page: 923
  year: 2007
  ident: 10.1016/j.bbabio.2009.01.004_bib41
  article-title: Monoubiquitylation promotes mitochondrial p53 translocation
  publication-title: EMBO J.
  doi: 10.1038/sj.emboj.7601560
– volume: 312
  start-page: 1650
  year: 2006
  ident: 10.1016/j.bbabio.2009.01.004_bib32
  article-title: p53 regulates mitochondrial respiration
  publication-title: Science (New York, N.Y
  doi: 10.1126/science.1126863
– volume: 6
  start-page: 2048
  year: 2007
  ident: 10.1016/j.bbabio.2009.01.004_bib17
  article-title: Cell cycle- and ribonucleotide reductase-driven changes in mtDNA copy number influence mtDNA Inheritance without compromising mitochondrial gene expression
  publication-title: Cell Cycle (Georgetown, Tex)
  doi: 10.4161/cc.6.16.4572
– volume: 3
  start-page: 1763
  year: 1994
  ident: 10.1016/j.bbabio.2009.01.004_bib38
  article-title: Deficiency of the human mitochondrial transcription factor h-mtTFA in infantile mitochondrial myopathy is associated with mtDNA depletion
  publication-title: Hum. Mol. Genet.
  doi: 10.1093/hmg/3.10.1763
– volume: 63
  start-page: 3729
  year: 2003
  ident: 10.1016/j.bbabio.2009.01.004_bib28
  article-title: P53 physically interacts with mitochondrial transcription factor A and differentially regulates binding to damaged DNA
  publication-title: Cancer Res.
– volume: 172
  start-page: 1445
  year: 2008
  ident: 10.1016/j.bbabio.2009.01.004_bib1
  article-title: Expression and maintenance of mitochondrial DNA: new insights into human disease pathology
  publication-title: Am. J. Pathol.
  doi: 10.2353/ajpath.2008.071163
– volume: 117
  start-page: 2723
  year: 2007
  ident: 10.1016/j.bbabio.2009.01.004_bib4
  article-title: Ataxia-telangiectasia mutated kinase regulates ribonucleotide reductase and mitochondrial homeostasis
  publication-title: J. Clin. Invest.
  doi: 10.1172/JCI31604
– volume: 16
  start-page: 3010
  year: 2005
  ident: 10.1016/j.bbabio.2009.01.004_bib16
  article-title: The conserved Mec1/Rad53 nuclear checkpoint pathway regulates mitochondrial DNA copy number in Saccharomyces cerevisiae
  publication-title: Mol. Biol. Cell
  doi: 10.1091/mbc.E05-01-0053
– volume: 303
  start-page: 1010
  year: 2004
  ident: 10.1016/j.bbabio.2009.01.004_bib22
  article-title: Direct activation of Bax by p53 mediates mitochondrial membrane permeabilization and apoptosis
  publication-title: Science (New York, N.Y
  doi: 10.1126/science.1092734
– volume: 18
  start-page: 231
  year: 1998
  ident: 10.1016/j.bbabio.2009.01.004_bib35
  article-title: Mitochondrial transcription factor A is necessary for mtDNA maintenance and embryogenesis in mice
  publication-title: Nat. Genet.
  doi: 10.1038/ng0398-231
– volume: 59
  start-page: 131
  year: 2008
  ident: 10.1016/j.bbabio.2009.01.004_bib12
  article-title: Inherited mitochondrial diseases of DNA replication
  publication-title: Annu. Rev. Med.
  doi: 10.1146/annurev.med.59.053006.104646
– volume: 24
  start-page: 6728
  year: 2004
  ident: 10.1016/j.bbabio.2009.01.004_bib23
  article-title: In vivo mitochondrial p53 translocation triggers a rapid first wave of cell death in response to DNA damage that can precede p53 target gene activation
  publication-title: Mol. Cell. Biol.
  doi: 10.1128/MCB.24.15.6728-6741.2004
– volume: 66
  start-page: 3485
  year: 2006
  ident: 10.1016/j.bbabio.2009.01.004_bib25
  article-title: The p53 pathway promotes efficient mitochondrial DNA base excision repair in colorectal cancer cells
  publication-title: Cancer Res.
  doi: 10.1158/0008-5472.CAN-05-4103
– volume: 64
  start-page: 2350
  year: 2004
  ident: 10.1016/j.bbabio.2009.01.004_bib46
  article-title: p53-induced up-regulation of MnSOD and GPx but not catalase increases oxidative stress and apoptosis
  publication-title: Cancer Res.
  doi: 10.1158/0008-5472.CAN-2287-2
– volume: 39
  start-page: 359
  year: 2005
  ident: 10.1016/j.bbabio.2009.01.004_bib2
  article-title: A mitochondrial paradigm of metabolic and degenerative diseases, aging, and cancer: a dawn for evolutionary medicine
  publication-title: Annu. Rev. Genet.
  doi: 10.1146/annurev.genet.39.110304.095751
– volume: 35
  start-page: 7399
  year: 2007
  ident: 10.1016/j.bbabio.2009.01.004_bib3
  article-title: The ageing mitochondrial genome
  publication-title: Nucleic Acids Res.
  doi: 10.1093/nar/gkm635
– volume: 282
  start-page: 16820
  year: 2007
  ident: 10.1016/j.bbabio.2009.01.004_bib19
  article-title: p53R2-dependent ribonucleotide reduction provides deoxyribonucleotides in quiescent human fibroblasts in the absence of induced DNA damage
  publication-title: J. Biol. Chem.
  doi: 10.1074/jbc.M701310200
– volume: 552
  start-page: 335
  year: 2003
  ident: 10.1016/j.bbabio.2009.01.004_bib31
  article-title: Mitochondrial formation of reactive oxygen species
  publication-title: J. Physiol.
  doi: 10.1113/jphysiol.2003.049478
– volume: 65
  start-page: 3745
  year: 2005
  ident: 10.1016/j.bbabio.2009.01.004_bib49
  article-title: p53 translocation to mitochondria precedes its nuclear translocation and targets mitochondrial oxidative defense protein-manganese superoxide dismutase
  publication-title: Cancer Res.
  doi: 10.1158/0008-5472.CAN-04-3835
– volume: 23
  start-page: 797
  year: 2004
  ident: 10.1016/j.bbabio.2009.01.004_bib13
  article-title: Deoxyribonucleotides and disorders of mitochondrial DNA integrity
  publication-title: DNA Cell Biol.
  doi: 10.1089/dna.2004.23.797
– volume: 354
  start-page: 86
  year: 2005
  ident: 10.1016/j.bbabio.2009.01.004_bib15
  article-title: Differential involvement of the related DNA helicases Pif1p and Rrm3p in mtDNA point mutagenesis and stability
  publication-title: Gene
  doi: 10.1016/j.gene.2005.03.031
– volume: 15
  start-page: 635
  year: 2001
  ident: 10.1016/j.bbabio.2009.01.004_bib27
  article-title: Direct influence of the p53 tumor suppressor on mitochondrial biogenesis and function
  publication-title: FASEB J.
  doi: 10.1096/fj.00-0262com
– volume: 17
  start-page: 3822
  year: 2008
  ident: 10.1016/j.bbabio.2009.01.004_bib7
  article-title: Infantile-onset spinocerebellar ataxia and mitochondrial recessive ataxia syndrome are associated with neuronal complex I defect and mtDNA depletion
  publication-title: Hum. Mol. Genet.
  doi: 10.1093/hmg/ddn280
– volume: 30
  start-page: 1929
  year: 2002
  ident: 10.1016/j.bbabio.2009.01.004_bib37
  article-title: Modulation of mitochondrial transcription in response to mtDNA depletion and repletion in HeLa cells
  publication-title: Nucleic Acids Res.
  doi: 10.1093/nar/30.9.1929
– year: 1989
  ident: 10.1016/j.bbabio.2009.01.004_bib30
– volume: 17
  start-page: 286
  year: 2007
  ident: 10.1016/j.bbabio.2009.01.004_bib20
  article-title: p53: new roles in metabolism
  publication-title: Trends Cell Biol.
  doi: 10.1016/j.tcb.2007.04.004
– volume: 124
  start-page: 269
  year: 1956
  ident: 10.1016/j.bbabio.2009.01.004_bib50
  article-title: On respiratory impairment in cancer cells
  publication-title: Science (New York, N.Y
  doi: 10.1126/science.124.3215.269
– volume: 7
  start-page: 54
  year: 2008
  ident: 10.1016/j.bbabio.2009.01.004_bib43
  article-title: Resistance of mitochondrial p53 to dominant inhibition
  publication-title: Mol. Cancer
  doi: 10.1186/1476-4598-7-54
– volume: 275
  start-page: 16202
  year: 2000
  ident: 10.1016/j.bbabio.2009.01.004_bib40
  article-title: Death signal-induced localization of p53 protein to mitochondria. A potential role in apoptotic signaling
  publication-title: J. Biol. Chem.
  doi: 10.1074/jbc.275.21.16202
– volume: 11
  start-page: 1306
  year: 2005
  ident: 10.1016/j.bbabio.2009.01.004_bib44
  article-title: The antioxidant function of the p53 tumor suppressor
  publication-title: Nat. Med.
  doi: 10.1038/nm1320
– volume: 80
  start-page: 389
  year: 2002
  ident: 10.1016/j.bbabio.2009.01.004_bib6
  article-title: Depletion of the other genome-mitochondrial DNA depletion syndromes in humans
  publication-title: J. Mol. Med.
  doi: 10.1007/s00109-002-0343-5
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Snippet In addition to its central role in cellular stress signaling, the tumor suppressor p53 modulates mitochondrial respiration through its nuclear transcription...
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SubjectTerms Animals
Cancer
DNA Primers
DNA, Mitochondrial - genetics
Fibroblasts - cytology
Fibroblasts - physiology
Gene Deletion
Homeostasis
Humans
Membrane Potentials
Mice
Mice, Inbred C57BL
Mice, Knockout
Mitochondria - metabolism
Mitochondria - physiology
Mitochondrial transcription factor A
mtDNA depletion
Oxidative Phosphorylation
p53
p53R2
Polymerase Chain Reaction
Reactive oxygen species
Reactive Oxygen Species - metabolism
RNA, Messenger - genetics
Transcription, Genetic
Tumor Suppressor Protein p53 - deficiency
Tumor Suppressor Protein p53 - genetics
Title Loss of p53 causes mitochondrial DNA depletion and altered mitochondrial reactive oxygen species homeostasis
URI https://dx.doi.org/10.1016/j.bbabio.2009.01.004
https://www.ncbi.nlm.nih.gov/pubmed/19413947
https://www.proquest.com/docview/67211978
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