Absence of a gender gap in survival. An analysis of the Italian registry for cystic fibrosis in the paediatric age

The existence of gender-related differences since childhood in survival of cystic fibrosis (CF) patients has been recently challenged. We evaluated the effect of gender on survival of 2293 CF patients born after 01/01/1988, followed up by 29 CF centres until 31/12/2004 and recorded in the Italian Re...

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Veröffentlicht in:Journal of cystic fibrosis Jg. 10; H. 5; S. 313 - 317
Hauptverfasser: Viviani, Laura, Bossi, Anna, Assael, Baroukh Maurice
Format: Journal Article
Sprache:Englisch
Veröffentlicht: Netherlands Elsevier B.V 01.09.2011
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ISSN:1569-1993, 1873-5010, 1873-5010
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Abstract The existence of gender-related differences since childhood in survival of cystic fibrosis (CF) patients has been recently challenged. We evaluated the effect of gender on survival of 2293 CF patients born after 01/01/1988, followed up by 29 CF centres until 31/12/2004 and recorded in the Italian Registry for CF (IRCF). We observed similar annual mortality rates in females (3.59‰) and males (4.00‰), similar survival curves (log-rank test p = 0.64) and similar hazards of death (hazard ratio adjusted for presence of symptoms at diagnosis, meconium ileus, F508del mutation and age at diagnosis: 1.29, 95%CI: 0.60; 2.76). However, excess mortality due to CF was higher for females (5.9) than males (5.1). In our population CF females do not experience higher mortality than males but, due to the disease, they lose the expected survival advantage occurring in the general population at this age. We do not exclude, however, that differences in mortality will establish after adolescence.
AbstractList The existence of gender-related differences since childhood in survival of cystic fibrosis (CF) patients has been recently challenged. We evaluated the effect of gender on survival of 2293 CF patients born after 01/01/1988, followed up by 29 CF centres until 31/12/2004 and recorded in the Italian Registry for CF (IRCF). We observed similar annual mortality rates in females (3.59‰) and males (4.00‰), similar survival curves (log-rank test p = 0.64) and similar hazards of death (hazard ratio adjusted for presence of symptoms at diagnosis, meconium ileus, F508del mutation and age at diagnosis: 1.29, 95%CI: 0.60; 2.76). However, excess mortality due to CF was higher for females (5.9) than males (5.1). In our population CF females do not experience higher mortality than males but, due to the disease, they lose the expected survival advantage occurring in the general population at this age. We do not exclude, however, that differences in mortality will establish after adolescence.
The existence of gender-related differences since childhood in survival of cystic fibrosis (CF) patients has been recently challenged. We evaluated the effect of gender on survival of 2293 CF patients born after 01/01/1988, followed up by 29 CF centres until 31/12/2004 and recorded in the Italian Registry for CF (IRCF). We observed similar annual mortality rates in females (3.59‰) and males (4.00‰), similar survival curves (log-rank test p=0.64) and similar hazards of death (hazard ratio adjusted for presence of symptoms at diagnosis, meconium ileus, F508del mutation and age at diagnosis: 1.29, 95%CI: 0.60; 2.76). However, excess mortality due to CF was higher for females (5.9) than males (5.1). In our population CF females do not experience higher mortality than males but, due to the disease, they lose the expected survival advantage occurring in the general population at this age. We do not exclude, however, that differences in mortality will establish after adolescence.
The existence of gender-related differences since childhood in survival of cystic fibrosis (CF) patients has been recently challenged.BACKGROUNDThe existence of gender-related differences since childhood in survival of cystic fibrosis (CF) patients has been recently challenged.We evaluated the effect of gender on survival of 2293 CF patients born after 01/01/1988, followed up by 29 CF centres until 31/12/2004 and recorded in the Italian Registry for CF (IRCF).METHODSWe evaluated the effect of gender on survival of 2293 CF patients born after 01/01/1988, followed up by 29 CF centres until 31/12/2004 and recorded in the Italian Registry for CF (IRCF).We observed similar annual mortality rates in females (3.59‰) and males (4.00‰), similar survival curves (log-rank test p=0.64) and similar hazards of death (hazard ratio adjusted for presence of symptoms at diagnosis, meconium ileus, F508del mutation and age at diagnosis: 1.29, 95%CI: 0.60; 2.76). However, excess mortality due to CF was higher for females (5.9) than males (5.1).RESULTSWe observed similar annual mortality rates in females (3.59‰) and males (4.00‰), similar survival curves (log-rank test p=0.64) and similar hazards of death (hazard ratio adjusted for presence of symptoms at diagnosis, meconium ileus, F508del mutation and age at diagnosis: 1.29, 95%CI: 0.60; 2.76). However, excess mortality due to CF was higher for females (5.9) than males (5.1).In our population CF females do not experience higher mortality than males but, due to the disease, they lose the expected survival advantage occurring in the general population at this age. We do not exclude, however, that differences in mortality will establish after adolescence.CONCLUSIONSIn our population CF females do not experience higher mortality than males but, due to the disease, they lose the expected survival advantage occurring in the general population at this age. We do not exclude, however, that differences in mortality will establish after adolescence.
Abstract Background The existence of gender-related differences since childhood in survival of cystic fibrosis (CF) patients has been recently challenged. Methods We evaluated the effect of gender on survival of 2293 CF patients born after 01/01/1988, followed up by 29 CF centres until 31/12/2004 and recorded in the Italian Registry for CF (IRCF). Results We observed similar annual mortality rates in females (3.59‰) and males (4.00‰), similar survival curves (log-rank test p = 0.64) and similar hazards of death (hazard ratio adjusted for presence of symptoms at diagnosis, meconium ileus, F508del mutation and age at diagnosis: 1.29, 95%CI: 0.60; 2.76). However, excess mortality due to CF was higher for females (5.9) than males (5.1). Conclusions In our population CF females do not experience higher mortality than males but, due to the disease, they lose the expected survival advantage occurring in the general population at this age. We do not exclude, however, that differences in mortality will establish after adolescence.
Author Bossi, Anna
Viviani, Laura
Assael, Baroukh Maurice
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  surname: Viviani
  fullname: Viviani, Laura
  email: laura.viviani@unimi.it
  organization: Dipartimento di Medicina del Lavoro “Clinica del Lavoro L.Devoto”, Sezione di Statistica Medica e Biometria “G.A. Maccacaro”, Università degli Studi di Milano. Via Venezian 1, 20133 Milano, Italy
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  givenname: Anna
  surname: Bossi
  fullname: Bossi, Anna
  organization: Dipartimento di Medicina del Lavoro “Clinica del Lavoro L.Devoto”, Sezione di Statistica Medica e Biometria “G.A. Maccacaro”, Università degli Studi di Milano. Via Venezian 1, 20133 Milano, Italy
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  givenname: Baroukh Maurice
  surname: Assael
  fullname: Assael, Baroukh Maurice
  organization: Center for Cystic Fibrosis. Piazza Stefani 1, 37100 Verona, Italy
BackLink https://www.ncbi.nlm.nih.gov/pubmed/21514901$$D View this record in MEDLINE/PubMed
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Snippet The existence of gender-related differences since childhood in survival of cystic fibrosis (CF) patients has been recently challenged. We evaluated the effect...
Abstract Background The existence of gender-related differences since childhood in survival of cystic fibrosis (CF) patients has been recently challenged....
The existence of gender-related differences since childhood in survival of cystic fibrosis (CF) patients has been recently challenged.BACKGROUNDThe existence...
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StartPage 313
SubjectTerms Adolescent
Age Distribution
Child
Child, Preschool
Cystic Fibrosis - epidemiology
Female
Humans
Incidence
Infant
Italy - epidemiology
Kaplan-Meier Estimate
Longitudinal Studies
Male
Pulmonary/Respiratory
Registries - statistics & numerical data
Risk Factors
Sex Distribution
Title Absence of a gender gap in survival. An analysis of the Italian registry for cystic fibrosis in the paediatric age
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https://dx.doi.org/10.1016/j.jcf.2011.03.007
https://www.ncbi.nlm.nih.gov/pubmed/21514901
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