Structural cerebellar correlates of cognitive functions in spinocerebellar ataxia type 2

Spinocerebellar ataxia type 2 (SCA2) is an autosomal dominant neurodegenerative disease involving the cerebellum and characterized by a typical motor syndrome. In addition, the presence of cognitive impairment is now widely acknowledged as a feature of SCA2. Given the extensive connections between t...

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Published in:Journal of neurology Vol. 265; no. 3; pp. 597 - 606
Main Authors: Olivito, G., Lupo, M., Iacobacci, C., Clausi, S., Romano, S., Masciullo, M., Molinari, M., Cercignani, M., Bozzali, M., Leggio, M.
Format: Journal Article
Language:English
Published: Berlin/Heidelberg Springer Berlin Heidelberg 01.03.2018
Springer Nature B.V
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ISSN:0340-5354, 1432-1459, 1432-1459
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Abstract Spinocerebellar ataxia type 2 (SCA2) is an autosomal dominant neurodegenerative disease involving the cerebellum and characterized by a typical motor syndrome. In addition, the presence of cognitive impairment is now widely acknowledged as a feature of SCA2. Given the extensive connections between the cerebellum and associative cerebral areas, it is reasonable to hypothesize that cerebellar neurodegeneration associated with SCA2 may impact on the cerebellar modulation of the cerebral cortex, thus resulting in functional impairment. The aim of the present study was to investigate and quantitatively map the pattern of cerebellar gray matter (GM) atrophy due to SCA2 neurodegeneration and to correlate that with patients’ cognitive performances. Cerebellar GM maps were extracted and compared between SCA2 patients ( n  = 9) and controls ( n  = 33) by using voxel-based morphometry. Furthermore, the relationship between cerebellar GM atrophy and neuropsychological scores of the patients was assessed. Specific cerebellar GM regions were found to be affected in patients. Additionally, GM loss in cognitive posterior lobules (VI, Crus I, Crus II, VIIB, IX) correlated with visuospatial, verbal memory and executive tasks, while additional correlations with motor anterior (V) and posterior (VIIIA, VIIIB) lobules were found for the tasks engaging motor and planning components. Our results provide evidence that the SCA2 neurodegenerative process affects the cerebellar cortex and that MRI indices of atrophy in different cerebellar subregions may account for the specificity of cognitive symptomatology observed in patients, as result of a cerebello-cerebral dysregulation.
AbstractList Spinocerebellar ataxia type 2 (SCA2) is an autosomal dominant neurodegenerative disease involving the cerebellum and characterized by a typical motor syndrome. In addition, the presence of cognitive impairment is now widely acknowledged as a feature of SCA2. Given the extensive connections between the cerebellum and associative cerebral areas, it is reasonable to hypothesize that cerebellar neurodegeneration associated with SCA2 may impact on the cerebellar modulation of the cerebral cortex, thus resulting in functional impairment. The aim of the present study was to investigate and quantitatively map the pattern of cerebellar gray matter (GM) atrophy due to SCA2 neurodegeneration and to correlate that with patients’ cognitive performances. Cerebellar GM maps were extracted and compared between SCA2 patients (n = 9) and controls (n = 33) by using voxel-based morphometry. Furthermore, the relationship between cerebellar GM atrophy and neuropsychological scores of the patients was assessed. Specific cerebellar GM regions were found to be affected in patients. Additionally, GM loss in cognitive posterior lobules (VI, Crus I, Crus II, VIIB, IX) correlated with visuospatial, verbal memory and executive tasks, while additional correlations with motor anterior (V) and posterior (VIIIA, VIIIB) lobules were found for the tasks engaging motor and planning components. Our results provide evidence that the SCA2 neurodegenerative process affects the cerebellar cortex and that MRI indices of atrophy in different cerebellar subregions may account for the specificity of cognitive symptomatology observed in patients, as result of a cerebello-cerebral dysregulation.
Spinocerebellar ataxia type 2 (SCA2) is an autosomal dominant neurodegenerative disease involving the cerebellum and characterized by a typical motor syndrome. In addition, the presence of cognitive impairment is now widely acknowledged as a feature of SCA2. Given the extensive connections between the cerebellum and associative cerebral areas, it is reasonable to hypothesize that cerebellar neurodegeneration associated with SCA2 may impact on the cerebellar modulation of the cerebral cortex, thus resulting in functional impairment. The aim of the present study was to investigate and quantitatively map the pattern of cerebellar gray matter (GM) atrophy due to SCA2 neurodegeneration and to correlate that with patients’ cognitive performances. Cerebellar GM maps were extracted and compared between SCA2 patients ( n  = 9) and controls ( n  = 33) by using voxel-based morphometry. Furthermore, the relationship between cerebellar GM atrophy and neuropsychological scores of the patients was assessed. Specific cerebellar GM regions were found to be affected in patients. Additionally, GM loss in cognitive posterior lobules (VI, Crus I, Crus II, VIIB, IX) correlated with visuospatial, verbal memory and executive tasks, while additional correlations with motor anterior (V) and posterior (VIIIA, VIIIB) lobules were found for the tasks engaging motor and planning components. Our results provide evidence that the SCA2 neurodegenerative process affects the cerebellar cortex and that MRI indices of atrophy in different cerebellar subregions may account for the specificity of cognitive symptomatology observed in patients, as result of a cerebello-cerebral dysregulation.
Spinocerebellar ataxia type 2 (SCA2) is an autosomal dominant neurodegenerative disease involving the cerebellum and characterized by a typical motor syndrome. In addition, the presence of cognitive impairment is now widely acknowledged as a feature of SCA2. Given the extensive connections between the cerebellum and associative cerebral areas, it is reasonable to hypothesize that cerebellar neurodegeneration associated with SCA2 may impact on the cerebellar modulation of the cerebral cortex, thus resulting in functional impairment. The aim of the present study was to investigate and quantitatively map the pattern of cerebellar gray matter (GM) atrophy due to SCA2 neurodegeneration and to correlate that with patients' cognitive performances. Cerebellar GM maps were extracted and compared between SCA2 patients (n = 9) and controls (n = 33) by using voxel-based morphometry. Furthermore, the relationship between cerebellar GM atrophy and neuropsychological scores of the patients was assessed. Specific cerebellar GM regions were found to be affected in patients. Additionally, GM loss in cognitive posterior lobules (VI, Crus I, Crus II, VIIB, IX) correlated with visuospatial, verbal memory and executive tasks, while additional correlations with motor anterior (V) and posterior (VIIIA, VIIIB) lobules were found for the tasks engaging motor and planning components. Our results provide evidence that the SCA2 neurodegenerative process affects the cerebellar cortex and that MRI indices of atrophy in different cerebellar subregions may account for the specificity of cognitive symptomatology observed in patients, as result of a cerebello-cerebral dysregulation.Spinocerebellar ataxia type 2 (SCA2) is an autosomal dominant neurodegenerative disease involving the cerebellum and characterized by a typical motor syndrome. In addition, the presence of cognitive impairment is now widely acknowledged as a feature of SCA2. Given the extensive connections between the cerebellum and associative cerebral areas, it is reasonable to hypothesize that cerebellar neurodegeneration associated with SCA2 may impact on the cerebellar modulation of the cerebral cortex, thus resulting in functional impairment. The aim of the present study was to investigate and quantitatively map the pattern of cerebellar gray matter (GM) atrophy due to SCA2 neurodegeneration and to correlate that with patients' cognitive performances. Cerebellar GM maps were extracted and compared between SCA2 patients (n = 9) and controls (n = 33) by using voxel-based morphometry. Furthermore, the relationship between cerebellar GM atrophy and neuropsychological scores of the patients was assessed. Specific cerebellar GM regions were found to be affected in patients. Additionally, GM loss in cognitive posterior lobules (VI, Crus I, Crus II, VIIB, IX) correlated with visuospatial, verbal memory and executive tasks, while additional correlations with motor anterior (V) and posterior (VIIIA, VIIIB) lobules were found for the tasks engaging motor and planning components. Our results provide evidence that the SCA2 neurodegenerative process affects the cerebellar cortex and that MRI indices of atrophy in different cerebellar subregions may account for the specificity of cognitive symptomatology observed in patients, as result of a cerebello-cerebral dysregulation.
Spinocerebellar ataxia type 2 (SCA2) is an autosomal dominant neurodegenerative disease involving the cerebellum and characterized by a typical motor syndrome. In addition, the presence of cognitive impairment is now widely acknowledged as a feature of SCA2. Given the extensive connections between the cerebellum and associative cerebral areas, it is reasonable to hypothesize that cerebellar neurodegeneration associated with SCA2 may impact on the cerebellar modulation of the cerebral cortex, thus resulting in functional impairment. The aim of the present study was to investigate and quantitatively map the pattern of cerebellar gray matter (GM) atrophy due to SCA2 neurodegeneration and to correlate that with patients' cognitive performances. Cerebellar GM maps were extracted and compared between SCA2 patients (n = 9) and controls (n = 33) by using voxel-based morphometry. Furthermore, the relationship between cerebellar GM atrophy and neuropsychological scores of the patients was assessed. Specific cerebellar GM regions were found to be affected in patients. Additionally, GM loss in cognitive posterior lobules (VI, Crus I, Crus II, VIIB, IX) correlated with visuospatial, verbal memory and executive tasks, while additional correlations with motor anterior (V) and posterior (VIIIA, VIIIB) lobules were found for the tasks engaging motor and planning components. Our results provide evidence that the SCA2 neurodegenerative process affects the cerebellar cortex and that MRI indices of atrophy in different cerebellar subregions may account for the specificity of cognitive symptomatology observed in patients, as result of a cerebello-cerebral dysregulation.
Author Leggio, M.
Romano, S.
Cercignani, M.
Masciullo, M.
Bozzali, M.
Olivito, G.
Clausi, S.
Molinari, M.
Iacobacci, C.
Lupo, M.
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  organization: Ataxia Laborarory, IRCCS Santa Lucia Foundation, Neuroimaging Laboratory, IRCCS Santa Lucia Foundation
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BackLink https://www.ncbi.nlm.nih.gov/pubmed/29356974$$D View this record in MEDLINE/PubMed
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Cites_doi 10.1152/jn.00339.2011
10.1152/jn.00598.2012
10.1097/00001756-200310060-00008
10.1007/BF01997792
10.1001/archneur.56.1.43
10.1093/jmcb/mjq005
10.1016/S0022-510X(96)00231-6
10.2217/fnl.14.6
10.1007/s004010050989
10.1159/000117297
10.1007/s00415-013-7138-1
10.1016/S0074-7742(08)60346-3
10.1093/brain/aww348
10.1016/j.euroneuro.2010.03.008
10.3389/fnana.2016.00029
10.1159/000206850
10.1093/brain/118.6.1573
10.1093/brain/awr266
10.1098/rstb.1971.0106
10.1016/0028-3932(67)90015-2
10.1136/jnnp.69.1.102
10.1016/j.neuroimage.2008.08.039
10.1002/ana.410390214
10.1146/annurev.ph.31.030169.002315
10.1002/hbm.22194
10.1016/j.neuroscience.2009.02.001
10.1093/brain/awf060
10.1007/s12311-010-0183-8
10.1016/j.cortex.2009.11.008
10.1093/brain/121.4.561
10.1002/mds.21982
10.1016/j.neuroimage.2015.09.032
10.1093/cercor/bhp135
10.1016/j.neuroimage.2009.01.045
10.1016/j.neuroscience.2017.10.007
10.1016/j.nicl.2017.03.009
10.1523/JNEUROSCI.1868-09.2009
10.1016/j.nicl.2016.10.013
10.1186/s13023-016-0447-6
10.1007/s00415-003-0976-5
10.1016/S0022-510X(02)00194-6
10.1080/01688639408402697
10.1016/j.neuroimage.2005.06.013
10.1093/brain/awh729
10.1007/s100720200003
10.1523/JNEUROSCI.21-02-00700.2001
10.1007/s10072-012-1130-x
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ISSN 0340-5354
1432-1459
IngestDate Sun Nov 09 11:23:36 EST 2025
Tue Nov 04 23:11:30 EST 2025
Wed Feb 19 02:43:25 EST 2025
Sat Nov 29 02:48:27 EST 2025
Tue Nov 18 21:52:29 EST 2025
Fri Feb 21 02:41:46 EST 2025
IsDoiOpenAccess false
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Issue 3
Keywords Cerebellum
Atrophy
Voxel based morphometry
Cognition
Functional topography
SCA2
Language English
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OpenAccessLink https://figshare.com/articles/journal_contribution/Structural_cerebellar_correlates_of_cognitive_functions_in_spinocerebellar_ataxia_type_2/23454836
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PublicationTitle Journal of neurology
PublicationTitleAbbrev J Neurol
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Springer Nature B.V
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References Fancellu, Paridi, Tomasello, Panzeri, Castaldo, Genitrini, Soliveri, Girotti (CR9) 2013; 260
Tedesco, Chiricozzi, Clausi, Lupo, Molinari, Leggio (CR4) 2011; 134
Allen, McColl, Bernard, Ringe, Fleckenstein, Cullum (CR57) 2005; 28
Bernard, Seidler, Hassevoort, Benson, Welsh, Wiggins, Jaeggi, Buschkuehl, Monk, Jonides, Peltier (CR43) 2012; 10
Klinke, Minnerop, Schmitz-Hübsch, Hendriks, Klockgether, Wüllner, Helmstaedter (CR8) 2010; 9
Kawai, Suenaga, Watanabe, Sobue (CR20) 2009; 61
Caffarra, Vezzadini, Dieci, Zonato, Venneri (CR30) 2002; 22
CR36
Schmahmann, Pandya (CR54) 1997; 41
Olivito, Cercignani, Lupo, Iacobacci, Clausi, Romano, Masciullo, Molinari, Bozzali, Leggio (CR21) 2017; 14
Pang, Giunti, Chamberlain, An, Vitaliani, Scaravilli, Martinian, Wood, Scaravilli, Ansorge (CR15) 2002; 125
Borkowsky, Benton, Spreen (CR35) 1967; 5
Kemp, Powell (CR53) 1971; 262
Storey, Forrest, Shaw, Mitchell, Gardner (CR23) 1999; 56
Trouillas, Takayanagi, Hallett, Currier, Subramony, Wessel, Bryer, Diener, Massaquoi, Gomez, Coutinho, Ben Hamida, Campanella, Filla, Schut, Timann, Honnorat, Nighoghossian, Manyam (CR25) 1997; 145
Carlesimo, Caltagirone, Gainotti (CR34) 1996; 36
Iwabuchi, Tsuchiya, Uchihara, Yagishita (CR16) 1999; 155
Habas, Kamdar, Nguyen, Prater, Beckmann, Menon, Greicius (CR42) 2009; 29
Leggio, Silveri, Petrosini, Molinari (CR49) 2000; 69
Dayan, Olivito, Molinari, Cercignani, Bozzali, Leggio (CR17) 2016; 31
Stoodley, Schmahmann (CR40) 2009; 44
Stoodley, MacMore, Makris, Sherman, Schmahmann (CR44) 2016; 12
Durr, Smadja, Cancel, Lezin, Stevanin, Mikol (CR12) 1995; 118
Keren-Happuch, Chen, Ho, Desmond (CR51) 2014; 35
Spinnler, Tognoni (CR33) 1987; 8
Kansal, Yang, Fishman, Sair, Ying, Jedynak, Prince, Onyike (CR45) 2017; 140
Diedrichsen, Balsters, Flavell, Cussan, Ramnani (CR39) 2009; 46
Schmahmann, Sherman (CR2) 1998; 121
Krikorian, Bartok, Gay (CR37) 1994; 16
Clausi, Bozzali, Leggio, Di Paola, Hagberg, Caltagirone, Molinari (CR3) 2009; 162
van den Heuvel, Hulshoff Pol (CR48) 2010; 20
Corsi (CR31) 1972; 34
Schmahmann, Caplan (CR1) 2006; 129
Stoodley, Schmahmann (CR24) 2010; 46
Monaco, Costa, Caltagirone, Carlesimo (CR32) 2013
Buckner, Krienen, Castellanos, Diaz, Yeo (CR50) 2011; 106
Chopra, Shakkottai (CR6) 2014; 9
Takahashi, Katada, Onodera (CR7) 2010; 2
Giovagnoli, Del Pesce, Mascheroni, Simoncelli, Laiacona, Capitani (CR38) 1996; 17
Milardi, Arrigo, Anastasi, Cacciola, Marino, Mormina, Calamuneri, Bruschetta, Cutroneo, Trimarchi, Quartarone (CR58) 2016; 10
Moriarty, Cook, Hunt, Adams, Cipolotti, Giunti (CR10) 2016; 11
Middleton, Strick (CR56) 2001; 21
Estrada, Galarraga, Orozco, Nodarse, Auburger (CR13) 1999; 97
CR28
CR27
CR26
King, Hernandez-Castillo, Diedrichsen (CR47) 2017; 140
Raven (CR29) 1949
Della Nave, Ginestroni, Tessa, Cosottini, Giannelli, Salvatore, Sartucci, De Michele, Dotti, Piacentini, Mascalchi (CR11) 2008; 23
Bürk, Globas, BöschS, ZühlkeI, Daum, Dichgans (CR19) 2003; 250
Krienen, Buckner (CR41) 2009; 19
Yang, Ye, Bogovic, Carass, Jedynak, Ying (CR46) 2016; 127
Le Pira, Zappala, Saponara, Domina, Restivo, Reggio, Nicoletti, Giuffrida (CR22) 2002; 201
Olivito, Lupo, Iacobacci, Clausi, Romano, Masciullo, Molinari, Cercignani, Bozzali, Leggio (CR5) 2017; 366
Brenneis, Bosch, Schocke, Wenning, Poewe (CR18) 2003; 14
Evarts, Thach (CR52) 1969; 31
Gilman, Sima, Junck, Kluin, Koeppe, Lohman (CR14) 1996; 39
Wang, Buckner, Liu (CR55) 2013; 109
R Della Nave (8738_CR11) 2008; 23
K Iwabuchi (8738_CR16) 1999; 155
M Dayan (8738_CR17) 2016; 31
R Fancellu (8738_CR9) 2013; 260
FA Middleton (8738_CR56) 2001; 21
R Chopra (8738_CR6) 2014; 9
A Durr (8738_CR12) 1995; 118
8738_CR26
8738_CR27
G Olivito (8738_CR5) 2017; 366
8738_CR28
K Kansal (8738_CR45) 2017; 140
JC Raven (8738_CR29) 1949
CJ Stoodley (8738_CR24) 2010; 46
JT Pang (8738_CR15) 2002; 125
CJ Stoodley (8738_CR40) 2009; 44
R Estrada (8738_CR13) 1999; 97
G Allen (8738_CR57) 2005; 28
JD Schmahmann (8738_CR54) 1997; 41
JD Schmahmann (8738_CR1) 2006; 129
S Clausi (8738_CR3) 2009; 162
A Moriarty (8738_CR10) 2016; 11
JD Schmahmann (8738_CR2) 1998; 121
M Monaco (8738_CR32) 2013
MG Leggio (8738_CR49) 2000; 69
I Klinke (8738_CR8) 2010; 9
JG Borkowsky (8738_CR35) 1967; 5
C Habas (8738_CR42) 2009; 29
P Trouillas (8738_CR25) 1997; 145
E Storey (8738_CR23) 1999; 56
JA Bernard (8738_CR43) 2012; 10
T Takahashi (8738_CR7) 2010; 2
Z Yang (8738_CR46) 2016; 127
F Pira Le (8738_CR22) 2002; 201
R Krikorian (8738_CR37) 1994; 16
MP Heuvel van den (8738_CR48) 2010; 20
D Milardi (8738_CR58) 2016; 10
Y Kawai (8738_CR20) 2009; 61
EV Evarts (8738_CR52) 1969; 31
AM Tedesco (8738_CR4) 2011; 134
E Keren-Happuch (8738_CR51) 2014; 35
J Diedrichsen (8738_CR39) 2009; 46
P Caffarra (8738_CR30) 2002; 22
PM Corsi (8738_CR31) 1972; 34
AR Giovagnoli (8738_CR38) 1996; 17
M King (8738_CR47) 2017; 140
GA Carlesimo (8738_CR34) 1996; 36
S Gilman (8738_CR14) 1996; 39
8738_CR36
C Brenneis (8738_CR18) 2003; 14
D Wang (8738_CR55) 2013; 109
FM Krienen (8738_CR41) 2009; 19
RL Buckner (8738_CR50) 2011; 106
CJ Stoodley (8738_CR44) 2016; 12
K Bürk (8738_CR19) 2003; 250
JM Kemp (8738_CR53) 1971; 262
G Olivito (8738_CR21) 2017; 14
H Spinnler (8738_CR33) 1987; 8
References_xml – volume: 106
  start-page: 2322
  year: 2011
  end-page: 2345
  ident: CR50
  article-title: The organization of the human cerebellum estimated by intrinsic functional connectivity
  publication-title: J Neurophysiol
  doi: 10.1152/jn.00339.2011
– volume: 109
  start-page: 46
  issue: 1
  year: 2013
  end-page: 57
  ident: CR55
  article-title: Cerebellar asymmetry and its relation to cerebral asymmetry estimated by intrinsic functional connectivity
  publication-title: J Neurophysiol
  doi: 10.1152/jn.00598.2012
– volume: 14
  start-page: 1799
  year: 2003
  end-page: 1802
  ident: CR18
  article-title: Atrophy pattern in SCA2 determined by voxel-based morphometry
  publication-title: NeuroReport
  doi: 10.1097/00001756-200310060-00008
– volume: 17
  start-page: 305
  year: 1996
  end-page: 309
  ident: CR38
  article-title: Trail making test: normative values from 287 normal adult controls
  publication-title: Ital J Neurol Sci
  doi: 10.1007/BF01997792
– volume: 56
  start-page: 43
  issue: 1
  year: 1999
  end-page: 50
  ident: CR23
  article-title: Spinocerebellar ataxia type 2: clinical features of a pedigree displaying prominent frontal-executive dysfunction
  publication-title: Arch Neurol
  doi: 10.1001/archneur.56.1.43
– volume: 2
  start-page: 180
  year: 2010
  end-page: 191
  ident: CR7
  article-title: Polyglutamine diseases: where does toxicity come from? What is toxicity? Where are we going?
  publication-title: J Mol Cell Biol
  doi: 10.1093/jmcb/mjq005
– volume: 145
  start-page: 205
  year: 1997
  end-page: 211
  ident: CR25
  article-title: International cooperative ataxia rating scale for pharmacological assessment of the cerebellar syndrome. The Ataxia Neuropharmacology Committee of the World Federation of Neurology
  publication-title: J Neurol Sci
  doi: 10.1016/S0022-510X(96)00231-6
– volume: 9
  start-page: 187
  year: 2014
  end-page: 196
  ident: CR6
  article-title: Translating cerebellar Purkinje neuron physiology to progress in dominantly inherited ataxia
  publication-title: Futur Neurol
  doi: 10.2217/fnl.14.6
– volume: 97
  start-page: 306
  year: 1999
  end-page: 310
  ident: CR13
  article-title: Spinocerebellar ataxia 2 (SCA2),: morphometric analyses in 11 autopsies
  publication-title: Acta Neuropathol (Berl)
  doi: 10.1007/s004010050989
– volume: 140
  start-page: 707
  issue: 3
  year: 2017
  end-page: 720
  ident: CR45
  article-title: Structural cerebellar correlates of cognitive and motor dysfunctions in cerebellar degeneration
  publication-title: Brain
– year: 2013
  ident: CR32
  article-title: Forward and backward span for verbal and visuo-spatial data: standardization and normative data from an Italian adult population
  publication-title: Neurol Sci
– volume: 36
  start-page: 378
  issue: 6
  year: 1996
  end-page: 384
  ident: CR34
  article-title: The mental deterioration battery: normative data, diagnostic reliability and qualitative analyses of cognitive impairment. The Group for the Standardization of the Mental Deterioration Battery
  publication-title: Eur Neurol
  doi: 10.1159/000117297
– volume: 260
  start-page: 3134
  year: 2013
  end-page: 3143
  ident: CR9
  article-title: Longitudinal study of cognitive and psychiatric functions in spinocerebellar ataxia types 1 and 2
  publication-title: J Neurol
  doi: 10.1007/s00415-013-7138-1
– volume: 34
  start-page: 891
  year: 1972
  ident: CR31
  article-title: Human memory and the medial temporal regions of the brain
  publication-title: Dissert Abst Int
– volume: 31
  start-page: 239
  issue: 4
  year: 2016
  end-page: 248
  ident: CR17
  article-title: Impact of cerebellar atrophy on cortical gray matter and cerebellar peduncles as assessed by voxel-based morphometry and high angular resolution diffusion imaging
  publication-title: Funct Neurol
– volume: 41
  start-page: 31
  year: 1997
  end-page: 60
  ident: CR54
  article-title: The cerebrocerebellar system
  publication-title: Int Rev Neurobiol
  doi: 10.1016/S0074-7742(08)60346-3
– volume: 140
  start-page: 522
  issue: 3
  year: 2017
  end-page: 524
  ident: CR47
  article-title: Towards a multi-function mapping of the cerebellar cortex
  publication-title: Brain
  doi: 10.1093/brain/aww348
– volume: 20
  start-page: 519
  year: 2010
  end-page: 534
  ident: CR48
  article-title: Exploring the brain network, a review on resting-state fMRI functional connectivity
  publication-title: Eur Neuropsychopharmacol
  doi: 10.1016/j.euroneuro.2010.03.008
– volume: 10
  start-page: 29
  year: 2016
  ident: CR58
  article-title: Extensive direct subcortical cerebellum-basal ganglia connections in human brain as revealed by constrained spherical deconvolution tractography
  publication-title: Front Neuroanat
  doi: 10.3389/fnana.2016.00029
– volume: 61
  start-page: 257
  year: 2009
  end-page: 268
  ident: CR20
  article-title: Cognitive impairment in spinocerebellar degeneration
  publication-title: Eur Neurol
  doi: 10.1159/000206850
– volume: 118
  start-page: 1573
  year: 1995
  end-page: 1581
  ident: CR12
  article-title: Autosomal dominant cerebellar ataxia type I in Martinique (French West Indies), Clinical and neuropathological analysis of 53 patients from three unrelated SCA2 families
  publication-title: Brain
  doi: 10.1093/brain/118.6.1573
– volume: 134
  start-page: 3672
  year: 2011
  end-page: 3686
  ident: CR4
  article-title: The cerebellar cognitive profile
  publication-title: Brain
  doi: 10.1093/brain/awr266
– volume: 262
  start-page: 441
  year: 1971
  end-page: 457
  ident: CR53
  article-title: The connexions of the striatum and globus pallidus: synthesis and speculation
  publication-title: Philos Trans R Soc Lond B Biol Sci
  doi: 10.1098/rstb.1971.0106
– volume: 5
  start-page: 135
  year: 1967
  end-page: 140
  ident: CR35
  article-title: Word fluency and brain-damage
  publication-title: Neuropsychologia
  doi: 10.1016/0028-3932(67)90015-2
– volume: 69
  start-page: 102
  year: 2000
  end-page: 106
  ident: CR49
  article-title: Phonological grouping is specifically affected in cerebellar patients: a verbal fluency study
  publication-title: J Neurol Neurosurg Psychiatry
  doi: 10.1136/jnnp.69.1.102
– ident: CR36
– volume: 44
  start-page: 489
  year: 2009
  end-page: 501
  ident: CR40
  article-title: Functional topography in the human cerebellum: a meta-analysis of neuroimaging studies
  publication-title: Neuroimage
  doi: 10.1016/j.neuroimage.2008.08.039
– volume: 39
  start-page: 241
  year: 1996
  end-page: 255
  ident: CR14
  article-title: Spinocerebellar ataxia type1 with multiple system degeneration and glial cytoplasmic inclusions
  publication-title: Ann Neurol
  doi: 10.1002/ana.410390214
– volume: 31
  start-page: 451
  year: 1969
  end-page: 498
  ident: CR52
  article-title: Motor mechanisms of the CNS: cerebrocerebellar interrelations
  publication-title: Annu Rev Physiol
  doi: 10.1146/annurev.ph.31.030169.002315
– ident: CR26
– volume: 35
  start-page: 593
  year: 2014
  end-page: 615
  ident: CR51
  article-title: A meta-analysis of cerebellar contributions to higher cognition from PET and fMRI studies
  publication-title: Hum Brain Mapp
  doi: 10.1002/hbm.22194
– volume: 162
  start-page: 827
  issue: 3
  year: 2009
  end-page: 835
  ident: CR3
  article-title: Quantification of gray matter changes in the cerebral cortex after isolated cerebellar damage: a voxel-based morphometry study
  publication-title: Neuroscience
  doi: 10.1016/j.neuroscience.2009.02.001
– volume: 125
  start-page: 656
  year: 2002
  end-page: 663
  ident: CR15
  article-title: Neuronal intranuclear inclusions in SCA2: a genetic, morphological and immunohistochemical study of two cases
  publication-title: Brain
  doi: 10.1093/brain/awf060
– volume: 9
  start-page: 433
  year: 2010
  end-page: 442
  ident: CR8
  article-title: Neuropsychological features of patients with Spinocerebellar ataxia (SCA), types 1,2,3, and 6
  publication-title: Cerebellum
  doi: 10.1007/s12311-010-0183-8
– volume: 46
  start-page: 831
  issue: 7
  year: 2010
  end-page: 844
  ident: CR24
  article-title: Evidence for topographic organization in the cerebellum of motor control versus cognitive and affective processing
  publication-title: Cortex
  doi: 10.1016/j.cortex.2009.11.008
– volume: 121
  start-page: 561
  year: 1998
  end-page: 579
  ident: CR2
  article-title: The cerebellar cognitive affective syndrome
  publication-title: Brain
  doi: 10.1093/brain/121.4.561
– volume: 8
  start-page: 1
  issue: Suppl
  year: 1987
  end-page: 120
  ident: CR33
  article-title: Standardizzazione e taratura italiana di test neuropsicologici
  publication-title: Ital J Neurol Sci
– volume: 23
  start-page: 899
  issue: 6
  year: 2008
  end-page: 903
  ident: CR11
  article-title: Brain structural damage in spinocerebellar ataxia type 2. A voxel-based morphometry study
  publication-title: Mov Disord
  doi: 10.1002/mds.21982
– volume: 127
  start-page: 435
  year: 2016
  end-page: 444
  ident: CR46
  article-title: Automated cerebellar lobule segmentation with application to cerebellar structural analysis in cerebellar disease
  publication-title: Neuroimage
  doi: 10.1016/j.neuroimage.2015.09.032
– volume: 10
  start-page: 6
  year: 2012
  end-page: 31
  ident: CR43
  article-title: Resting state functional connectivity networks: a comparison of anatomical and self-organizing map approaches
  publication-title: Front Neuroanat
– year: 1949
  ident: CR29
  publication-title: Progressive matrices, Sets A, Ab, B: Board and Book forms
– volume: 19
  start-page: 2485
  issue: 10
  year: 2009
  end-page: 2497
  ident: CR41
  article-title: Segregated fronto-cerebellar circuits revealed by intrinsic functional connectivity
  publication-title: Cereb Cortex
  doi: 10.1093/cercor/bhp135
– volume: 46
  start-page: 39
  year: 2009
  end-page: 46
  ident: CR39
  article-title: A probabilistic atlas of the human cerebellum
  publication-title: Neuroimage
  doi: 10.1016/j.neuroimage.2009.01.045
– ident: CR27
– volume: 366
  start-page: 44
  year: 2017
  end-page: 53
  ident: CR5
  article-title: Microstructural MRI basis of the cognitive functions in patients with Spinocerebellar ataxia type 2
  publication-title: Neuroscience
  doi: 10.1016/j.neuroscience.2017.10.007
– volume: 14
  start-page: 719
  year: 2017
  end-page: 725
  ident: CR21
  article-title: Neural substrates of motor and cognitive dysfunctions in SCA2 patients: a network based statistics analysis
  publication-title: Neuroimage Clin
  doi: 10.1016/j.nicl.2017.03.009
– volume: 29
  start-page: 8586
  year: 2009
  end-page: 8594
  ident: CR42
  article-title: Distinct cerebellar contributions to intrinsic connectivity networks
  publication-title: J Neurosci
  doi: 10.1523/JNEUROSCI.1868-09.2009
– volume: 12
  start-page: 765
  year: 2016
  end-page: 775
  ident: CR44
  article-title: Location of lesion determines motor vs. cognitive consequences in patients with cerebellar stroke
  publication-title: Neuroimage Clin
  doi: 10.1016/j.nicl.2016.10.013
– volume: 11
  start-page: 82
  year: 2016
  ident: CR10
  article-title: A longitudinal investigation into cognition and disease progression in spinocerebellar ataxia types 1, 2, 3, 6, and 7
  publication-title: Orphanet J Rare Dis
  doi: 10.1186/s13023-016-0447-6
– volume: 250
  start-page: 207
  year: 2003
  end-page: 211
  ident: CR19
  article-title: Cognitive deficits in spinocerebellar ataxia type 1, 2, and 3
  publication-title: J Neurol
  doi: 10.1007/s00415-003-0976-5
– volume: 201
  start-page: 53
  year: 2002
  end-page: 57
  ident: CR22
  article-title: Cognitive findings in spinocerebellar ataxia type 2: relationship to genetic and clinical variables
  publication-title: J Neurol Sci
  doi: 10.1016/S0022-510X(02)00194-6
– volume: 16
  start-page: 840
  issue: 6
  year: 1994
  end-page: 850
  ident: CR37
  article-title: Tower of London procedure: a standard method and developmental data
  publication-title: J Clin Exp Neuropsychol
  doi: 10.1080/01688639408402697
– volume: 28
  start-page: 39
  year: 2005
  end-page: 48
  ident: CR57
  article-title: Magnetic Resonance Imaging of cerebellar-prefrontal and cerebellar parietal functional connectivity
  publication-title: Neuroimage
  doi: 10.1016/j.neuroimage.2005.06.013
– volume: 155
  start-page: 255
  year: 1999
  end-page: 270
  ident: CR16
  article-title: Autosomal dominant spinocerebellar degenerations. Clinical, pathological, and genetic correlations
  publication-title: Rev Neurol (Paris)
– ident: CR28
– volume: 129
  start-page: 290
  issue: Pt 2
  year: 2006
  end-page: 292
  ident: CR1
  article-title: Cognition, emotion and the cerebellum
  publication-title: Brain
  doi: 10.1093/brain/awh729
– volume: 22
  start-page: 443
  year: 2002
  end-page: 447
  ident: CR30
  article-title: Rey–Osterrieth complex figure: normative values in an Italian population sample
  publication-title: Neurol Sci
  doi: 10.1007/s100720200003
– volume: 21
  start-page: 700
  year: 2001
  end-page: 712
  ident: CR56
  article-title: Cerebellar projections to the prefrontal cortex of the primate
  publication-title: J Neurosci
– volume: 155
  start-page: 255
  year: 1999
  ident: 8738_CR16
  publication-title: Rev Neurol (Paris)
– volume: 145
  start-page: 205
  year: 1997
  ident: 8738_CR25
  publication-title: J Neurol Sci
  doi: 10.1016/S0022-510X(96)00231-6
– volume: 39
  start-page: 241
  year: 1996
  ident: 8738_CR14
  publication-title: Ann Neurol
  doi: 10.1002/ana.410390214
– volume: 127
  start-page: 435
  year: 2016
  ident: 8738_CR46
  publication-title: Neuroimage
  doi: 10.1016/j.neuroimage.2015.09.032
– volume: 250
  start-page: 207
  year: 2003
  ident: 8738_CR19
  publication-title: J Neurol
  doi: 10.1007/s00415-003-0976-5
– volume: 29
  start-page: 8586
  year: 2009
  ident: 8738_CR42
  publication-title: J Neurosci
  doi: 10.1523/JNEUROSCI.1868-09.2009
– volume: 2
  start-page: 180
  year: 2010
  ident: 8738_CR7
  publication-title: J Mol Cell Biol
  doi: 10.1093/jmcb/mjq005
– volume: 36
  start-page: 378
  issue: 6
  year: 1996
  ident: 8738_CR34
  publication-title: Eur Neurol
  doi: 10.1159/000117297
– volume: 9
  start-page: 433
  year: 2010
  ident: 8738_CR8
  publication-title: Cerebellum
  doi: 10.1007/s12311-010-0183-8
– volume: 121
  start-page: 561
  year: 1998
  ident: 8738_CR2
  publication-title: Brain
  doi: 10.1093/brain/121.4.561
– volume: 162
  start-page: 827
  issue: 3
  year: 2009
  ident: 8738_CR3
  publication-title: Neuroscience
  doi: 10.1016/j.neuroscience.2009.02.001
– volume: 21
  start-page: 700
  year: 2001
  ident: 8738_CR56
  publication-title: J Neurosci
  doi: 10.1523/JNEUROSCI.21-02-00700.2001
– year: 2013
  ident: 8738_CR32
  publication-title: Neurol Sci
  doi: 10.1007/s10072-012-1130-x
– volume: 31
  start-page: 451
  year: 1969
  ident: 8738_CR52
  publication-title: Annu Rev Physiol
  doi: 10.1146/annurev.ph.31.030169.002315
– volume: 35
  start-page: 593
  year: 2014
  ident: 8738_CR51
  publication-title: Hum Brain Mapp
  doi: 10.1002/hbm.22194
– volume: 201
  start-page: 53
  year: 2002
  ident: 8738_CR22
  publication-title: J Neurol Sci
  doi: 10.1016/S0022-510X(02)00194-6
– volume: 134
  start-page: 3672
  year: 2011
  ident: 8738_CR4
  publication-title: Brain
  doi: 10.1093/brain/awr266
– volume: 56
  start-page: 43
  issue: 1
  year: 1999
  ident: 8738_CR23
  publication-title: Arch Neurol
  doi: 10.1001/archneur.56.1.43
– volume: 9
  start-page: 187
  year: 2014
  ident: 8738_CR6
  publication-title: Futur Neurol
  doi: 10.2217/fnl.14.6
– volume: 97
  start-page: 306
  year: 1999
  ident: 8738_CR13
  publication-title: Acta Neuropathol (Berl)
  doi: 10.1007/s004010050989
– volume: 31
  start-page: 239
  issue: 4
  year: 2016
  ident: 8738_CR17
  publication-title: Funct Neurol
– volume-title: Progressive matrices, Sets A, Ab, B: Board and Book forms
  year: 1949
  ident: 8738_CR29
– volume: 14
  start-page: 719
  year: 2017
  ident: 8738_CR21
  publication-title: Neuroimage Clin
  doi: 10.1016/j.nicl.2017.03.009
– volume: 46
  start-page: 39
  year: 2009
  ident: 8738_CR39
  publication-title: Neuroimage
  doi: 10.1016/j.neuroimage.2009.01.045
– volume: 129
  start-page: 290
  issue: Pt 2
  year: 2006
  ident: 8738_CR1
  publication-title: Brain
  doi: 10.1093/brain/awh729
– volume: 46
  start-page: 831
  issue: 7
  year: 2010
  ident: 8738_CR24
  publication-title: Cortex
  doi: 10.1016/j.cortex.2009.11.008
– volume: 22
  start-page: 443
  year: 2002
  ident: 8738_CR30
  publication-title: Neurol Sci
  doi: 10.1007/s100720200003
– volume: 11
  start-page: 82
  year: 2016
  ident: 8738_CR10
  publication-title: Orphanet J Rare Dis
  doi: 10.1186/s13023-016-0447-6
– volume: 125
  start-page: 656
  year: 2002
  ident: 8738_CR15
  publication-title: Brain
  doi: 10.1093/brain/awf060
– ident: 8738_CR26
– volume: 61
  start-page: 257
  year: 2009
  ident: 8738_CR20
  publication-title: Eur Neurol
  doi: 10.1159/000206850
– volume: 23
  start-page: 899
  issue: 6
  year: 2008
  ident: 8738_CR11
  publication-title: Mov Disord
  doi: 10.1002/mds.21982
– volume: 262
  start-page: 441
  year: 1971
  ident: 8738_CR53
  publication-title: Philos Trans R Soc Lond B Biol Sci
  doi: 10.1098/rstb.1971.0106
– volume: 10
  start-page: 29
  year: 2016
  ident: 8738_CR58
  publication-title: Front Neuroanat
  doi: 10.3389/fnana.2016.00029
– volume: 34
  start-page: 891
  year: 1972
  ident: 8738_CR31
  publication-title: Dissert Abst Int
– volume: 10
  start-page: 6
  year: 2012
  ident: 8738_CR43
  publication-title: Front Neuroanat
– volume: 19
  start-page: 2485
  issue: 10
  year: 2009
  ident: 8738_CR41
  publication-title: Cereb Cortex
  doi: 10.1093/cercor/bhp135
– volume: 106
  start-page: 2322
  year: 2011
  ident: 8738_CR50
  publication-title: J Neurophysiol
  doi: 10.1152/jn.00339.2011
– volume: 28
  start-page: 39
  year: 2005
  ident: 8738_CR57
  publication-title: Neuroimage
  doi: 10.1016/j.neuroimage.2005.06.013
– volume: 5
  start-page: 135
  year: 1967
  ident: 8738_CR35
  publication-title: Neuropsychologia
  doi: 10.1016/0028-3932(67)90015-2
– volume: 140
  start-page: 707
  issue: 3
  year: 2017
  ident: 8738_CR45
  publication-title: Brain
– ident: 8738_CR36
– ident: 8738_CR27
– volume: 44
  start-page: 489
  year: 2009
  ident: 8738_CR40
  publication-title: Neuroimage
  doi: 10.1016/j.neuroimage.2008.08.039
– volume: 17
  start-page: 305
  year: 1996
  ident: 8738_CR38
  publication-title: Ital J Neurol Sci
  doi: 10.1007/BF01997792
– volume: 140
  start-page: 522
  issue: 3
  year: 2017
  ident: 8738_CR47
  publication-title: Brain
  doi: 10.1093/brain/aww348
– volume: 20
  start-page: 519
  year: 2010
  ident: 8738_CR48
  publication-title: Eur Neuropsychopharmacol
  doi: 10.1016/j.euroneuro.2010.03.008
– volume: 8
  start-page: 1
  issue: Suppl
  year: 1987
  ident: 8738_CR33
  publication-title: Ital J Neurol Sci
– volume: 366
  start-page: 44
  year: 2017
  ident: 8738_CR5
  publication-title: Neuroscience
  doi: 10.1016/j.neuroscience.2017.10.007
– volume: 109
  start-page: 46
  issue: 1
  year: 2013
  ident: 8738_CR55
  publication-title: J Neurophysiol
  doi: 10.1152/jn.00598.2012
– volume: 41
  start-page: 31
  year: 1997
  ident: 8738_CR54
  publication-title: Int Rev Neurobiol
  doi: 10.1016/S0074-7742(08)60346-3
– volume: 118
  start-page: 1573
  year: 1995
  ident: 8738_CR12
  publication-title: Brain
  doi: 10.1093/brain/118.6.1573
– volume: 69
  start-page: 102
  year: 2000
  ident: 8738_CR49
  publication-title: J Neurol Neurosurg Psychiatry
  doi: 10.1136/jnnp.69.1.102
– ident: 8738_CR28
– volume: 12
  start-page: 765
  year: 2016
  ident: 8738_CR44
  publication-title: Neuroimage Clin
  doi: 10.1016/j.nicl.2016.10.013
– volume: 260
  start-page: 3134
  year: 2013
  ident: 8738_CR9
  publication-title: J Neurol
  doi: 10.1007/s00415-013-7138-1
– volume: 14
  start-page: 1799
  year: 2003
  ident: 8738_CR18
  publication-title: NeuroReport
  doi: 10.1097/00001756-200310060-00008
– volume: 16
  start-page: 840
  issue: 6
  year: 1994
  ident: 8738_CR37
  publication-title: J Clin Exp Neuropsychol
  doi: 10.1080/01688639408402697
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Snippet Spinocerebellar ataxia type 2 (SCA2) is an autosomal dominant neurodegenerative disease involving the cerebellum and characterized by a typical motor syndrome....
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SubjectTerms Ataxia
Atrophy
Cerebellum
Cerebral cortex
Cognitive ability
Magnetic resonance imaging
Medicine
Medicine & Public Health
Morphometry
Neurodegeneration
Neurology
Neuroradiology
Neurosciences
Original Communication
Spatial memory
Spinocerebellar ataxia
Substantia grisea
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Title Structural cerebellar correlates of cognitive functions in spinocerebellar ataxia type 2
URI https://link.springer.com/article/10.1007/s00415-018-8738-6
https://www.ncbi.nlm.nih.gov/pubmed/29356974
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