Combined Inhibition of EZH2 and FGFR is Synergistic in BAP1-deficient Malignant Mesothelioma

Malignant mesothelioma is a highly aggressive tumor with a survival of only 4-18 months after diagnosis. Treatment options for this disease are limited. Immune checkpoint blockade using ipilimumab and nivolumab has recently been approved as a frontline therapy, but this led to only a small improveme...

Ausführliche Beschreibung

Gespeichert in:
Bibliographische Detailangaben
Veröffentlicht in:Cancer research communications Jg. 4; H. 1; S. 18 - 27
Hauptverfasser: Badhai, Jitendra, Landman, Nick, Pandey, Gaurav Kumar, Song, Ji-Ying, Hulsman, Danielle, Krijgsman, Oscar, Chandrasekaran, Gayathri, Berns, Anton, van Lohuizen, Maarten
Format: Journal Article
Sprache:Englisch
Veröffentlicht: United States American Association for Cancer Research 03.01.2024
Schlagworte:
ISSN:2767-9764, 2767-9764
Online-Zugang:Volltext
Tags: Tag hinzufügen
Keine Tags, Fügen Sie den ersten Tag hinzu!
Abstract Malignant mesothelioma is a highly aggressive tumor with a survival of only 4-18 months after diagnosis. Treatment options for this disease are limited. Immune checkpoint blockade using ipilimumab and nivolumab has recently been approved as a frontline therapy, but this led to only a small improvement in overall patient survival. As more than half of patients with mesothelioma have alterations in the gene encoding for BAP1 this could be a potential marker for targeted therapies. In this study, we investigated the synergistic potential of combining EZH2 inhibition together with FGFR inhibition for treatment of BAP1-deficient malignancies. The efficacy of the combination was evaluated using human and murine preclinical models of mesothelioma and uveal melanoma in vitro. The efficacy of the combination was further validated in vivo by using BAP1-deficient mesothelioma xenografts and autochthonous mouse models. In vitro data showed sensitivity to the combined inhibition in BAP1-deficient mesothelioma and uveal melanoma tumor cell lines but not for BAP1-proficient subtypes. In vivo data showed susceptibility to the combination of BAP1-deficient xenografts and demonstrated an increase of survival in autochthonous models of mesothelioma. These results highlight the potential of this novel drug combination for the treatment of mesothelioma using BAP1 as a biomarker. Given these encouraging preclinical results, it will be important to clinically explore dual EZH2/FGFR inhibition in patients with BAP1-deficient malignant mesothelioma and justify further exploration in other BAP1 loss-associated tumors. Despite the recent approval of immunotherapy, malignant mesothelioma has limited treatment options and poor prognosis. Here, we observe that EZH2 inhibitors dramatically enhance the efficacy of FGFR inhibition, sensitising BAP1-mutant mesothelioma and uveal melanoma cells. The striking synergy of EZH2 and FGFR inhibition supports clinical investigations for BAP1-mutant tumors.
AbstractList Malignant mesothelioma is a highly aggressive tumor with a survival of only 4-18 months after diagnosis. Treatment options for this disease are limited. Immune checkpoint blockade using ipilimumab and nivolumab has recently been approved as a frontline therapy, but this led to only a small improvement in overall patient survival. As more than half of patients with mesothelioma have alterations in the gene encoding for BAP1 this could be a potential marker for targeted therapies. In this study, we investigated the synergistic potential of combining EZH2 inhibition together with FGFR inhibition for treatment of BAP1-deficient malignancies. The efficacy of the combination was evaluated using human and murine preclinical models of mesothelioma and uveal melanoma in vitro. The efficacy of the combination was further validated in vivo by using BAP1-deficient mesothelioma xenografts and autochthonous mouse models. In vitro data showed sensitivity to the combined inhibition in BAP1-deficient mesothelioma and uveal melanoma tumor cell lines but not for BAP1-proficient subtypes. In vivo data showed susceptibility to the combination of BAP1-deficient xenografts and demonstrated an increase of survival in autochthonous models of mesothelioma. These results highlight the potential of this novel drug combination for the treatment of mesothelioma using BAP1 as a biomarker. Given these encouraging preclinical results, it will be important to clinically explore dual EZH2/FGFR inhibition in patients with BAP1-deficient malignant mesothelioma and justify further exploration in other BAP1 loss-associated tumors. Despite the recent approval of immunotherapy, malignant mesothelioma has limited treatment options and poor prognosis. Here, we observe that EZH2 inhibitors dramatically enhance the efficacy of FGFR inhibition, sensitising BAP1-mutant mesothelioma and uveal melanoma cells. The striking synergy of EZH2 and FGFR inhibition supports clinical investigations for BAP1-mutant tumors.
Malignant mesothelioma is a highly aggressive tumor with a survival of only 4-18 months after diagnosis. Treatment options for this disease are limited. Immune checkpoint blockade using ipilimumab and nivolumab has recently been approved as a frontline therapy, but this led to only a small improvement in overall patient survival. As more than half of patients with mesothelioma have alterations in the gene encoding for BAP1 this could be a potential marker for targeted therapies. In this study, we investigated the synergistic potential of combining EZH2 inhibition together with FGFR inhibition for treatment of BAP1-deficient malignancies. The efficacy of the combination was evaluated using human and murine preclinical models of mesothelioma and uveal melanoma in vitro. The efficacy of the combination was further validated in vivo by using BAP1-deficient mesothelioma xenografts and autochthonous mouse models. In vitro data showed sensitivity to the combined inhibition in BAP1-deficient mesothelioma and uveal melanoma tumor cell lines but not for BAP1-proficient subtypes. In vivo data showed susceptibility to the combination of BAP1-deficient xenografts and demonstrated an increase of survival in autochthonous models of mesothelioma. These results highlight the potential of this novel drug combination for the treatment of mesothelioma using BAP1 as a biomarker. Given these encouraging preclinical results, it will be important to clinically explore dual EZH2/FGFR inhibition in patients with BAP1-deficient malignant mesothelioma and justify further exploration in other BAP1 loss-associated tumors.Malignant mesothelioma is a highly aggressive tumor with a survival of only 4-18 months after diagnosis. Treatment options for this disease are limited. Immune checkpoint blockade using ipilimumab and nivolumab has recently been approved as a frontline therapy, but this led to only a small improvement in overall patient survival. As more than half of patients with mesothelioma have alterations in the gene encoding for BAP1 this could be a potential marker for targeted therapies. In this study, we investigated the synergistic potential of combining EZH2 inhibition together with FGFR inhibition for treatment of BAP1-deficient malignancies. The efficacy of the combination was evaluated using human and murine preclinical models of mesothelioma and uveal melanoma in vitro. The efficacy of the combination was further validated in vivo by using BAP1-deficient mesothelioma xenografts and autochthonous mouse models. In vitro data showed sensitivity to the combined inhibition in BAP1-deficient mesothelioma and uveal melanoma tumor cell lines but not for BAP1-proficient subtypes. In vivo data showed susceptibility to the combination of BAP1-deficient xenografts and demonstrated an increase of survival in autochthonous models of mesothelioma. These results highlight the potential of this novel drug combination for the treatment of mesothelioma using BAP1 as a biomarker. Given these encouraging preclinical results, it will be important to clinically explore dual EZH2/FGFR inhibition in patients with BAP1-deficient malignant mesothelioma and justify further exploration in other BAP1 loss-associated tumors.Despite the recent approval of immunotherapy, malignant mesothelioma has limited treatment options and poor prognosis. Here, we observe that EZH2 inhibitors dramatically enhance the efficacy of FGFR inhibition, sensitising BAP1-mutant mesothelioma and uveal melanoma cells. The striking synergy of EZH2 and FGFR inhibition supports clinical investigations for BAP1-mutant tumors.SIGNIFICANCEDespite the recent approval of immunotherapy, malignant mesothelioma has limited treatment options and poor prognosis. Here, we observe that EZH2 inhibitors dramatically enhance the efficacy of FGFR inhibition, sensitising BAP1-mutant mesothelioma and uveal melanoma cells. The striking synergy of EZH2 and FGFR inhibition supports clinical investigations for BAP1-mutant tumors.
Malignant mesothelioma is a highly aggressive tumor with a survival of only 4–18 months after diagnosis. Treatment options for this disease are limited. Immune checkpoint blockade using ipilimumab and nivolumab has recently been approved as a frontline therapy, but this led to only a small improvement in overall patient survival. As more than half of patients with mesothelioma have alterations in the gene encoding for BAP1 this could be a potential marker for targeted therapies. In this study, we investigated the synergistic potential of combining EZH2 inhibition together with FGFR inhibition for treatment of BAP1-deficient malignancies. The efficacy of the combination was evaluated using human and murine preclinical models of mesothelioma and uveal melanoma in vitro. The efficacy of the combination was further validated in vivo by using BAP1-deficient mesothelioma xenografts and autochthonous mouse models. In vitro data showed sensitivity to the combined inhibition in BAP1-deficient mesothelioma and uveal melanoma tumor cell lines but not for BAP1-proficient subtypes. In vivo data showed susceptibility to the combination of BAP1-deficient xenografts and demonstrated an increase of survival in autochthonous models of mesothelioma. These results highlight the potential of this novel drug combination for the treatment of mesothelioma using BAP1 as a biomarker. Given these encouraging preclinical results, it will be important to clinically explore dual EZH2/FGFR inhibition in patients with BAP1-deficient malignant mesothelioma and justify further exploration in other BAP1 loss–associated tumors.
Author van Lohuizen, Maarten
Berns, Anton
Badhai, Jitendra
Hulsman, Danielle
Krijgsman, Oscar
Song, Ji-Ying
Pandey, Gaurav Kumar
Chandrasekaran, Gayathri
Landman, Nick
AuthorAffiliation 3 Department of Zoology, Banaras Hindu University, Varanasi, India
4 Department of Experimental Animal Pathology, The Netherlands Cancer Institute, Plesmanlaan, Amsterdam, the Netherlands
2 Oncode Institute, Jaarbeursplein, Utrecht, the Netherlands
1 Division of Molecular Genetics, The Netherlands Cancer Institute, Plesmanlaan, Amsterdam, the Netherlands
5 Division of Molecular Oncology and Immunology, The Netherlands Cancer Institute, Plesmanlaan, Amsterdam, the Netherlands
AuthorAffiliation_xml – name: 4 Department of Experimental Animal Pathology, The Netherlands Cancer Institute, Plesmanlaan, Amsterdam, the Netherlands
– name: 2 Oncode Institute, Jaarbeursplein, Utrecht, the Netherlands
– name: 1 Division of Molecular Genetics, The Netherlands Cancer Institute, Plesmanlaan, Amsterdam, the Netherlands
– name: 5 Division of Molecular Oncology and Immunology, The Netherlands Cancer Institute, Plesmanlaan, Amsterdam, the Netherlands
– name: 3 Department of Zoology, Banaras Hindu University, Varanasi, India
Author_xml – sequence: 1
  givenname: Jitendra
  orcidid: 0000-0002-9526-3748
  surname: Badhai
  fullname: Badhai, Jitendra
– sequence: 2
  givenname: Nick
  orcidid: 0000-0001-9473-4686
  surname: Landman
  fullname: Landman, Nick
– sequence: 3
  givenname: Gaurav Kumar
  orcidid: 0000-0002-4372-9331
  surname: Pandey
  fullname: Pandey, Gaurav Kumar
– sequence: 4
  givenname: Ji-Ying
  orcidid: 0000-0002-6296-1996
  surname: Song
  fullname: Song, Ji-Ying
– sequence: 5
  givenname: Danielle
  orcidid: 0000-0001-9347-8553
  surname: Hulsman
  fullname: Hulsman, Danielle
– sequence: 6
  givenname: Oscar
  orcidid: 0000-0003-0825-3291
  surname: Krijgsman
  fullname: Krijgsman, Oscar
– sequence: 7
  givenname: Gayathri
  orcidid: 0009-0009-8276-2562
  surname: Chandrasekaran
  fullname: Chandrasekaran, Gayathri
– sequence: 8
  givenname: Anton
  orcidid: 0000-0003-2194-1988
  surname: Berns
  fullname: Berns, Anton
– sequence: 9
  givenname: Maarten
  orcidid: 0000-0001-6877-2873
  surname: van Lohuizen
  fullname: van Lohuizen, Maarten
BackLink https://www.ncbi.nlm.nih.gov/pubmed/38054839$$D View this record in MEDLINE/PubMed
BookMark eNqFkUtv1TAQhS1URB_0J4C8ZJPiZ-yIBSpRb1upFajABiFZju3cOyixS5xbqf8eRy1XhU1XHs2cc2bk7xDtxRQDQm8oOaFU6vdM1apqVC1O2pu2YrwipfMCHez6e0_qfXSc8y9CikYJWfNXaJ9rIoXmzQH62aaxgxg8vowb6GCGFHHq8dmPC4Zt9Hh1vrrBkPHX-ximNeQZHIaIP51-oZUPPTgIccbXdoB1tEsVcpo3YYA02tfoZW-HHI4f3yP0fXX2rb2orj6fX7anV5UTVMxVz5xzoWNSBSW8lLL2XjvSk5oFLQJXnIpOWOm0ZZKoXnrqCLHa-4bQhnh-hD4-5N5uuzF4Vy6a7GBuJxjtdG-SBfPvJMLGrNOdoUTVXHJSEt49Jkzp9zbk2YyQXRgGG0PaZsN0oxspakKL9O3TZbstf_-0COSDwE0p5yn0OwklZsFnFjRmQWMKPsO4WfAV34f_fA5muwApN8PwjPsPYaOfvw
CitedBy_id crossref_primary_10_3390_cancers16111971
crossref_primary_10_3390_cancers17091581
crossref_primary_10_1038_s41571_024_00972_1
crossref_primary_10_1016_j_bbcan_2025_189267
Cites_doi 10.1016/S0140-6736(20)32714-8
10.1038/nrc2736
10.1016/S1470-2045(22)00277-7
10.1186/s13059-014-0550-8
10.1038/232054a0
10.1158/1078-0432.CCR-21-1466
10.1016/0166-3542(90)90001-N
10.1158/1078-0432.CCR-17-1172
10.1038/nrm4067
10.1371/journal.pone.0092444
10.1073/pnas.0806213105
10.1097/JTO.0000000000000471
10.1016/j.lungcan.2019.12.018
10.1016/j.lungcan.2016.12.004
10.1016/S0140-6736(10)60251-6
10.1186/1479-5876-10-179
10.1016/j.xcrm.2022.100915
10.1038/nm.3947
10.1084/jem.20191257
10.1038/modpathol.2016.188
10.1016/j.jtho.2016.12.019
10.1038/ng.855
10.1038/nature08966
10.1038/nrc1991
10.1200/JCO.2022.40.16_suppl.3122
10.1038/ng.912
10.1126/science.2168090
10.1056/NEJMra050152
10.1016/j.lungcan.2012.02.022
10.1038/ng.3520
ContentType Journal Article
Copyright 2024 The Authors; Published by the American Association for Cancer Research.
2024 The Authors; Published by the American Association for Cancer Research 2024 Copyright held by the owner/author(s).
Copyright_xml – notice: 2024 The Authors; Published by the American Association for Cancer Research.
– notice: 2024 The Authors; Published by the American Association for Cancer Research 2024 Copyright held by the owner/author(s).
DBID AAYXX
CITATION
CGR
CUY
CVF
ECM
EIF
NPM
7X8
5PM
DOI 10.1158/2767-9764.CRC-23-0276
DatabaseName CrossRef
Medline
MEDLINE
MEDLINE (Ovid)
MEDLINE
MEDLINE
PubMed
MEDLINE - Academic
PubMed Central (Full Participant titles)
DatabaseTitle CrossRef
MEDLINE
Medline Complete
MEDLINE with Full Text
PubMed
MEDLINE (Ovid)
MEDLINE - Academic
DatabaseTitleList MEDLINE
MEDLINE - Academic

Database_xml – sequence: 1
  dbid: NPM
  name: PubMed
  url: http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=PubMed
  sourceTypes: Index Database
– sequence: 2
  dbid: 7X8
  name: MEDLINE - Academic
  url: https://search.proquest.com/medline
  sourceTypes: Aggregation Database
DeliveryMethod fulltext_linktorsrc
Discipline Medicine
DocumentTitleAlternate Inhibition of EZH2 and FGFR Synergizes in BAP1-deficient MM
EISSN 2767-9764
EndPage 27
ExternalDocumentID PMC10763530
38054839
10_1158_2767_9764_CRC_23_0276
Genre Research Support, Non-U.S. Gov't
Journal Article
GrantInformation_xml – fundername: Oncode Institute
  grantid: P2019
– fundername: KWF Kankerbestrijding (DCS)
  grantid: KWF,Grant # 11700
– fundername: EC | European Research Council (ERC)
  grantid: 319661 COMBATCANCER
– fundername: ;
  grantid: P2019
– fundername: ;
  grantid: KWF,Grant # 11700
– fundername: ;
  grantid: 319661 COMBATCANCER
GroupedDBID 53G
AAYXX
ALMA_UNASSIGNED_HOLDINGS
CITATION
EBS
GROUPED_DOAJ
M~E
OK1
RCR
RPM
W2D
CGR
CUY
CVF
ECM
EIF
NPM
7X8
5PM
ID FETCH-LOGICAL-c414t-f2ccceb257e74d5556dd8c0f062e84e37314b4a5c8a2507f5d1c00a8dd90190d3
ISICitedReferencesCount 4
ISICitedReferencesURI http://www.webofscience.com/api/gateway?GWVersion=2&SrcApp=Summon&SrcAuth=ProQuest&DestLinkType=CitingArticles&DestApp=WOS_CPL&KeyUT=001154251800002&url=https%3A%2F%2Fcvtisr.summon.serialssolutions.com%2F%23%21%2Fsearch%3Fho%3Df%26include.ft.matches%3Dt%26l%3Dnull%26q%3D
ISSN 2767-9764
IngestDate Tue Sep 30 17:10:26 EDT 2025
Thu Jul 10 17:02:01 EDT 2025
Thu Apr 03 07:04:32 EDT 2025
Sat Nov 29 02:19:46 EST 2025
Tue Nov 18 20:44:36 EST 2025
IsDoiOpenAccess true
IsOpenAccess true
IsPeerReviewed true
IsScholarly true
Issue 1
Language English
License 2024 The Authors; Published by the American Association for Cancer Research.
This open access article is distributed under the Creative Commons Attribution 4.0 International (CC BY 4.0) license.
LinkModel OpenURL
MergedId FETCHMERGED-LOGICAL-c414t-f2ccceb257e74d5556dd8c0f062e84e37314b4a5c8a2507f5d1c00a8dd90190d3
Notes ObjectType-Article-1
SourceType-Scholarly Journals-1
ObjectType-Feature-2
content type line 23
J. Badhai and N. Landman Contributed equally to this article.
ORCID 0000-0002-4372-9331
0000-0003-2194-1988
0000-0002-9526-3748
0000-0003-0825-3291
0000-0001-9473-4686
0000-0001-6877-2873
0009-0009-8276-2562
0000-0001-9347-8553
0000-0002-6296-1996
OpenAccessLink http://dx.doi.org/10.1158/2767-9764.CRC-23-0276
PMID 38054839
PQID 2898954601
PQPubID 23479
PageCount 10
ParticipantIDs pubmedcentral_primary_oai_pubmedcentral_nih_gov_10763530
proquest_miscellaneous_2898954601
pubmed_primary_38054839
crossref_primary_10_1158_2767_9764_CRC_23_0276
crossref_citationtrail_10_1158_2767_9764_CRC_23_0276
PublicationCentury 2000
PublicationDate 2024-01-03
PublicationDateYYYYMMDD 2024-01-03
PublicationDate_xml – month: 01
  year: 2024
  text: 2024-01-03
  day: 03
PublicationDecade 2020
PublicationPlace United States
PublicationPlace_xml – name: United States
PublicationTitle Cancer research communications
PublicationTitleAlternate Cancer Res Commun
PublicationYear 2024
Publisher American Association for Cancer Research
Publisher_xml – name: American Association for Cancer Research
References Cheng (2024010314073775100_bib13) 1994; 54
Bott (2024010314073775100_bib16) 2011; 43
Nasu (2024010314073775100_bib14) 2015; 10
Laurie (2024010314073775100_bib26) 2017; 104
Badhai (2024010314073775100_bib23) 2020; 217
Herold (2024010314073775100_bib29) 2008; 105
Lam (2024010314073775100_bib27) 2020; 140
Love (2024010314073775100_bib32) 2014; 15
Quispel-Janssen (2024010314073775100_bib7) 2018; 24
Guzman (2024010314073775100_bib31) 2014; 9
Prichard (2024010314073775100_bib30) 1990; 14
Robinson (2024010314073775100_bib3) 2005; 353
Cedres (2024010314073775100_bib9) 2012; 77
Testa (2024010314073775100_bib17) 2011; 43
Blackledge (2024010314073775100_bib19) 2015; 16
George (2024010314073775100_bib33) 2022; 40
Nakajima (2024010314073775100_bib5) 2022; 28
McDonald (2024010314073775100_bib2) 1990; 249
Joseph (2024010314073775100_bib11) 2017; 30
Suzuki (2024010314073775100_bib10) 2009; 2
Sekido (2024010314073775100_bib12) 1995; 55
Bracken (2024010314073775100_bib22) 2009; 9
LaFave (2024010314073775100_bib25) 2015; 21
Burki (2024010314073775100_bib4) 2010; 375
Scheuermann (2024010314073775100_bib20) 2010; 465
Bueno (2024010314073775100_bib8) 2016; 48
Baas (2024010314073775100_bib6) 2021; 397
Leblay (2024010314073775100_bib15) 2017; 12
Sparmann (2024010314073775100_bib21) 2006; 6
Pandey (2024010314073775100_bib24) 2023; 4
Harrington (2024010314073775100_bib1) 1971; 232
Zauderer (2024010314073775100_bib28) 2022; 23
Carbone (2024010314073775100_bib18) 2012; 10
References_xml – volume: 397
  start-page: 375
  year: 2021
  ident: 2024010314073775100_bib6
  article-title: First-line nivolumab plus ipilimumab in unresectable malignant pleural mesothelioma (CheckMate 743): a multicentre, randomised, open-label, phase 3 trial
  publication-title: Lancet
  doi: 10.1016/S0140-6736(20)32714-8
– volume: 9
  start-page: 773
  year: 2009
  ident: 2024010314073775100_bib22
  article-title: Polycomb group proteins: navigators of lineage pathways led astray in cancer
  publication-title: Nat Rev Cancer
  doi: 10.1038/nrc2736
– volume: 23
  start-page: 758
  year: 2022
  ident: 2024010314073775100_bib28
  article-title: EZH2 inhibitor tazemetostat in patients with relapsed or refractory, BAP1-inactivated malignant pleural mesothelioma: a multicentre, open-label, phase 2 study
  publication-title: Lancet Oncol
  doi: 10.1016/S1470-2045(22)00277-7
– volume: 15
  start-page: 550
  year: 2014
  ident: 2024010314073775100_bib32
  article-title: Moderated estimation of fold change and dispersion for RNA-seq data with DESeq2
  publication-title: Genome Biol
  doi: 10.1186/s13059-014-0550-8
– volume: 232
  start-page: 54
  year: 1971
  ident: 2024010314073775100_bib1
  article-title: Asbestos and mesothelioma in man
  publication-title: Nature
  doi: 10.1038/232054a0
– volume: 28
  start-page: 446
  year: 2022
  ident: 2024010314073775100_bib5
  article-title: FDA approval summary: nivolumab in combination with ipilimumab for the treatment of unresectable malignant pleural mesothelioma
  publication-title: Clin Cancer Res
  doi: 10.1158/1078-0432.CCR-21-1466
– volume: 14
  start-page: 181
  year: 1990
  ident: 2024010314073775100_bib30
  article-title: A three-dimensional model to analyze drug-drug interactions
  publication-title: Antiviral Res
  doi: 10.1016/0166-3542(90)90001-N
– volume: 54
  start-page: 5547
  year: 1994
  ident: 2024010314073775100_bib13
  article-title: p16 alterations and deletion mapping of 9p21-p22 in malignant mesothelioma
  publication-title: Cancer Res
– volume: 24
  start-page: 84
  year: 2018
  ident: 2024010314073775100_bib7
  article-title: Comprehensive pharmacogenomic profiling of malignant pleural mesothelioma identifies a subgroup sensitive to FGFR inhibition
  publication-title: Clin Cancer Res
  doi: 10.1158/1078-0432.CCR-17-1172
– volume: 16
  start-page: 643
  year: 2015
  ident: 2024010314073775100_bib19
  article-title: Targeting Polycomb systems to regulate gene expression: modifications to a complex story
  publication-title: Nat Rev Mol Cell Biol
  doi: 10.1038/nrm4067
– volume: 9
  start-page: e92444
  year: 2014
  ident: 2024010314073775100_bib31
  article-title: ColonyArea: an ImageJ plugin to automatically quantify colony formation in clonogenic assays
  publication-title: PLoS One
  doi: 10.1371/journal.pone.0092444
– volume: 105
  start-page: 18507
  year: 2008
  ident: 2024010314073775100_bib29
  article-title: Inducible and reversible gene silencing by stable integration of an shRNA-encoding lentivirus in transgenic rats
  publication-title: Proc Natl Acad Sci U S A
  doi: 10.1073/pnas.0806213105
– volume: 10
  start-page: 565
  year: 2015
  ident: 2024010314073775100_bib14
  article-title: High incidence of somatic BAP1 alterations in sporadic malignant mesothelioma
  publication-title: J Thorac Oncol
  doi: 10.1097/JTO.0000000000000471
– volume: 2
  start-page: 181
  year: 2009
  ident: 2024010314073775100_bib10
  article-title: Activation of the PI3K-AKT pathway in human malignant mesothelioma cells
  publication-title: Mol Med Rep
– volume: 140
  start-page: 87
  year: 2020
  ident: 2024010314073775100_bib27
  article-title: A phase II trial of single oral FGF inhibitor, AZD4547, as second or third line therapy in malignant pleural mesothelioma
  publication-title: Lung Cancer
  doi: 10.1016/j.lungcan.2019.12.018
– volume: 104
  start-page: 65
  year: 2017
  ident: 2024010314073775100_bib26
  article-title: A phase II trial of dovitinib in previously-treated advanced pleural mesothelioma: the Ontario clinical oncology group
  publication-title: Lung Cancer
  doi: 10.1016/j.lungcan.2016.12.004
– volume: 375
  start-page: 626
  year: 2010
  ident: 2024010314073775100_bib4
  article-title: Health experts concerned over India's asbestos industry
  publication-title: Lancet
  doi: 10.1016/S0140-6736(10)60251-6
– volume: 10
  start-page: 179
  year: 2012
  ident: 2024010314073775100_bib18
  article-title: BAP1 cancer syndrome: malignant mesothelioma, uveal and cutaneous melanoma, and MBAITs
  publication-title: J Transl Med
  doi: 10.1186/1479-5876-10-179
– volume: 4
  start-page: 100915
  year: 2023
  ident: 2024010314073775100_bib24
  article-title: Genetic screens reveal new targetable vulnerabilities in BAP1-deficient mesothelioma
  publication-title: Cell Rep Med
  doi: 10.1016/j.xcrm.2022.100915
– volume: 21
  start-page: 1344
  year: 2015
  ident: 2024010314073775100_bib25
  article-title: Loss of BAP1 function leads to EZH2-dependent transformation
  publication-title: Nat Med
  doi: 10.1038/nm.3947
– volume: 217
  start-page: e2019157
  year: 2020
  ident: 2024010314073775100_bib23
  article-title: Combined deletion of Bap1, Nf2, and Cdkn2ab causes rapid onset of malignant mesothelioma in mice
  publication-title: J Exp Med
  doi: 10.1084/jem.20191257
– volume: 30
  start-page: 246
  year: 2017
  ident: 2024010314073775100_bib11
  article-title: Genomic profiling of malignant peritoneal mesothelioma reveals recurrent alterations in epigenetic regulatory genes BAP1, SETD2, and DDX3X
  publication-title: Mod Pathol
  doi: 10.1038/modpathol.2016.188
– volume: 12
  start-page: 724
  year: 2017
  ident: 2024010314073775100_bib15
  article-title: BAP1 is altered by copy number loss, mutation, and/or loss of protein expression in more than 70% of malignant peritoneal mesotheliomas
  publication-title: J Thorac Oncol
  doi: 10.1016/j.jtho.2016.12.019
– volume: 43
  start-page: 668
  year: 2011
  ident: 2024010314073775100_bib16
  article-title: The nuclear deubiquitinase BAP1 is commonly inactivated by somatic mutations and 3p21.1 losses in malignant pleural mesothelioma
  publication-title: Nat Genet
  doi: 10.1038/ng.855
– volume: 465
  start-page: 243
  year: 2010
  ident: 2024010314073775100_bib20
  article-title: Histone H2A deubiquitinase activity of the polycomb repressive complex PR-DUB
  publication-title: Nature
  doi: 10.1038/nature08966
– volume: 6
  start-page: 846
  year: 2006
  ident: 2024010314073775100_bib21
  article-title: Polycomb silencers control cell fate, development and cancer
  publication-title: Nat Rev Cancer
  doi: 10.1038/nrc1991
– volume: 40
  year: 2022
  ident: 2024010314073775100_bib33
  article-title: Results of a phase II trial of the PARP inhibitor, niraparib, in BAP1 and other DNA damage response pathway deficient neoplasms
  publication-title: J Clin Oncol
  doi: 10.1200/JCO.2022.40.16_suppl.3122
– volume: 43
  start-page: 1022
  year: 2011
  ident: 2024010314073775100_bib17
  article-title: Germline BAP1 mutations predispose to malignant mesothelioma
  publication-title: Nat Genet
  doi: 10.1038/ng.912
– volume: 249
  start-page: 844
  year: 1990
  ident: 2024010314073775100_bib2
  article-title: Asbestos and carcinogenicity
  publication-title: Science
  doi: 10.1126/science.2168090
– volume: 353
  start-page: 1591
  year: 2005
  ident: 2024010314073775100_bib3
  article-title: Advances in malignant mesothelioma
  publication-title: N Engl J Med
  doi: 10.1056/NEJMra050152
– volume: 55
  start-page: 1227
  year: 1995
  ident: 2024010314073775100_bib12
  article-title: Neurofibromatosis type 2 (NF2) gene is somatically mutated in mesothelioma but not in lung cancer
  publication-title: Cancer Res
– volume: 77
  start-page: 192
  year: 2012
  ident: 2024010314073775100_bib9
  article-title: Exploratory analysis of activation of PTEN-PI3K pathway and downstream proteins in malignant pleural mesothelioma (MPM)
  publication-title: Lung Cancer
  doi: 10.1016/j.lungcan.2012.02.022
– volume: 48
  start-page: 407
  year: 2016
  ident: 2024010314073775100_bib8
  article-title: Comprehensive genomic analysis of malignant pleural mesothelioma identifies recurrent mutations, gene fusions and splicing alterations
  publication-title: Nat Genet
  doi: 10.1038/ng.3520
SSID ssj0002774563
Score 2.2704158
Snippet Malignant mesothelioma is a highly aggressive tumor with a survival of only 4-18 months after diagnosis. Treatment options for this disease are limited. Immune...
Malignant mesothelioma is a highly aggressive tumor with a survival of only 4–18 months after diagnosis. Treatment options for this disease are limited. Immune...
SourceID pubmedcentral
proquest
pubmed
crossref
SourceType Open Access Repository
Aggregation Database
Index Database
Enrichment Source
StartPage 18
SubjectTerms Animals
Biomarkers
Enhancer of Zeste Homolog 2 Protein - genetics
Humans
Lung Cancer
Lung Neoplasms - drug therapy
Melanoma - drug therapy
Mesothelioma - drug therapy
Mesothelioma, Malignant
Mice
Preclinical Models
Small Molecule Agents
Translational Research
Tumor Suppressor Proteins - genetics
Ubiquitin Thiolesterase - genetics
Title Combined Inhibition of EZH2 and FGFR is Synergistic in BAP1-deficient Malignant Mesothelioma
URI https://www.ncbi.nlm.nih.gov/pubmed/38054839
https://www.proquest.com/docview/2898954601
https://pubmed.ncbi.nlm.nih.gov/PMC10763530
Volume 4
WOSCitedRecordID wos001154251800002&url=https%3A%2F%2Fcvtisr.summon.serialssolutions.com%2F%23%21%2Fsearch%3Fho%3Df%26include.ft.matches%3Dt%26l%3Dnull%26q%3D
hasFullText 1
inHoldings 1
isFullTextHit
isPrint
journalDatabaseRights – providerCode: PRVAON
  databaseName: DOAJ Directory of Open Access Journals
  customDbUrl:
  eissn: 2767-9764
  dateEnd: 99991231
  omitProxy: false
  ssIdentifier: ssj0002774563
  issn: 2767-9764
  databaseCode: DOA
  dateStart: 20210101
  isFulltext: true
  titleUrlDefault: https://www.doaj.org/
  providerName: Directory of Open Access Journals
– providerCode: PRVHPJ
  databaseName: ROAD: Directory of Open Access Scholarly Resources
  customDbUrl:
  eissn: 2767-9764
  dateEnd: 99991231
  omitProxy: false
  ssIdentifier: ssj0002774563
  issn: 2767-9764
  databaseCode: M~E
  dateStart: 20210101
  isFulltext: true
  titleUrlDefault: https://road.issn.org
  providerName: ISSN International Centre
link http://cvtisr.summon.serialssolutions.com/2.0.0/link/0/eLvHCXMwtV1Lb9NAEF6lBVW9VLxJgWiRuEUu9nptr48lalqhJqpKQQEhWev1mloKTpSXyoUrf5uZ9SNOAwIOXCzLj7W13_jz7OzMt4S88sMgZszhlh-H3OIqCC3puMpyZRLr1AYX3dStfTgPhkMxGoUXrdaPqhZmNQ7yXNzchNP_CjUcA7CxdPYf4K4bhQOwD6DDFmCH7V8BD184jHY1ZvleZ3FWeYQnn86YmSnon_YvcRnzd9-w7M_oNGPQ483xhWMlGgUlMD1gAP75F0yS6Q70HKu0xtmkpPC1roHSs26pFoT5641Sk3XwXSblitdvMwy3z-rfwDm8TBl-HVbS_GYuK0-KMPqpXM7kqmuSwOtAUJVBnFkfq59uGbNg3MQsCh7ThttYAPwMnhBvEjHfsreCVAuC3uZ6D-sX6paOepc9i5lJab95PaAz_WqwdgX4p6LQTrolsl2d2iF3WOCFSI-D7-tgHQMn2fPdsgIMHvz6l4_dJ3tVQ5tuztbY5XYKbsOnubpHDsrBCD0ujOg-aen8AdkblOkWD8nnypbo2pboJKVoSxRwomhLNJvThi3RLKebtkRrW6JNW3pE3vdPrnpnVrkch6W4wxdWypRSOgaO1wFPPM_zk0QoO7V9pgXXbuA6PObSU0KCXx2kXuIo25YiSUIULEjcx2Q3n-T6KaHghUtbwVgCBfKE44fKT2MmHFdKT4ZctQmvei9SpVY9LpkyjsyY1RMR9n-E_R9B_0fMjbD_2-Sovm1aiLX86YaXFTQR0CrOlclcT5bziOGyqh73badNnhRQ1U1WGLeJ2ACxvgAl2zfP5Nm1kW53bBSAdO3D3zb6jOyvv5jnZHcxW-oX5K5aLbL5rEN2gpHomMBRx5joT9sYraY
linkProvider ISSN International Centre
openUrl ctx_ver=Z39.88-2004&ctx_enc=info%3Aofi%2Fenc%3AUTF-8&rfr_id=info%3Asid%2Fsummon.serialssolutions.com&rft_val_fmt=info%3Aofi%2Ffmt%3Akev%3Amtx%3Ajournal&rft.genre=article&rft.atitle=Combined+Inhibition+of+EZH2+and+FGFR+is+Synergistic+in+BAP1-deficient+Malignant+Mesothelioma&rft.jtitle=Cancer+research+communications&rft.au=Badhai%2C+Jitendra&rft.au=Landman%2C+Nick&rft.au=Pandey%2C+Gaurav+Kumar&rft.au=Song%2C+Ji-Ying&rft.date=2024-01-03&rft.eissn=2767-9764&rft.volume=4&rft.issue=1&rft.spage=18&rft_id=info:doi/10.1158%2F2767-9764.CRC-23-0276&rft_id=info%3Apmid%2F38054839&rft.externalDocID=38054839
thumbnail_l http://covers-cdn.summon.serialssolutions.com/index.aspx?isbn=/lc.gif&issn=2767-9764&client=summon
thumbnail_m http://covers-cdn.summon.serialssolutions.com/index.aspx?isbn=/mc.gif&issn=2767-9764&client=summon
thumbnail_s http://covers-cdn.summon.serialssolutions.com/index.aspx?isbn=/sc.gif&issn=2767-9764&client=summon