Safety and efficacy of pirfenidone and nintedanib in patients with idiopathic pulmonary fibrosis and carrying a telomere-related gene mutation

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Published in:The European respiratory journal Vol. 57; no. 2
Main Authors: Justet, Aurélien, Klay, Dymph, Porcher, Raphaël, Cottin, Vincent, Ahmad, Kais, Molina Molina, Maria, Nunes, Hilario, Reynaud-Gaubert, Martine, Naccache, Jean Marc, Manali, Effrosyni, Froidure, Antoine, Jouneau, Stéphane, Wemeau, Lidwine, Andrejak, Claire, Gondouin, Anne, Hirschi, Sandrine, Blanchard, Elodie, Bondue, Benjamin, Bonniaud, Philippe, Tromeur, Cécile, Prévot, Grégoire, Marchand-Adam, Sylvain, Funke-Chambour, Manuela, Gamez, Anne Sophie, Ba, Ibrahima, Papiris, Spyridon, Grutters, Jan, Crestani, Bruno, van Moorsel, Coline, Kannengiesser, Caroline, Borie, Raphaël
Format: Journal Article
Language:English
Published: England 01.02.2021
ISSN:1399-3003, 1399-3003
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Author Naccache, Jean Marc
Kannengiesser, Caroline
Manali, Effrosyni
Froidure, Antoine
Porcher, Raphaël
Papiris, Spyridon
Jouneau, Stéphane
Prévot, Grégoire
Wemeau, Lidwine
Blanchard, Elodie
Marchand-Adam, Sylvain
Tromeur, Cécile
Gamez, Anne Sophie
Ba, Ibrahima
Reynaud-Gaubert, Martine
Gondouin, Anne
van Moorsel, Coline
Bonniaud, Philippe
Nunes, Hilario
Crestani, Bruno
Hirschi, Sandrine
Cottin, Vincent
Molina Molina, Maria
Justet, Aurélien
Borie, Raphaël
Andrejak, Claire
Grutters, Jan
Funke-Chambour, Manuela
Ahmad, Kais
Bondue, Benjamin
Klay, Dymph
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  surname: Justet
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  organization: Center for rare pulmonary disease, Service de Pneumologie, CHU de Caen - ISTCT, UMR6030-CNRS-CEA-Université de Caen, Caen, France
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  givenname: Dymph
  surname: Klay
  fullname: Klay, Dymph
  organization: Interstitial Lung Diseases Center of Excellence, Dept of Pulmonology, St Antonius Hospital, Nieuwegein, The Netherlands
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  orcidid: 0000-0002-5277-4679
  surname: Porcher
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  organization: Centre of Research in Epidemiology and Statistics Sorbonne Paris Cité -CRESS-UMR1153, Paris, France
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  orcidid: 0000-0002-5591-0955
  surname: Cottin
  fullname: Cottin, Vincent
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  givenname: Kais
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  fullname: Ahmad, Kais
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  givenname: Maria
  surname: Molina Molina
  fullname: Molina Molina, Maria
  organization: Unit of Interstitial Lung Diseases, Dept of Pneumology, University Hospital of Bellvitge, Barcelona, Spain
– sequence: 7
  givenname: Hilario
  surname: Nunes
  fullname: Nunes, Hilario
  organization: Reference center for rare pulmonary diseases APHP, Service de Pneumologie, Hôpital Avicenne, Bobigny, France
– sequence: 8
  givenname: Martine
  surname: Reynaud-Gaubert
  fullname: Reynaud-Gaubert, Martine
  organization: Center for rare pulmonary disease, Service de Pneumologie, Hôpital Nord, Marseille, France
– sequence: 9
  givenname: Jean Marc
  surname: Naccache
  fullname: Naccache, Jean Marc
  organization: Reference center for rare pulmonary diseases, APHP, Service de Pneumologie, Hôpital Tenon, Paris, France
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  surname: Manali
  fullname: Manali, Effrosyni
  organization: Respiratory Medicine Dept, 'Attikon' University Hospital, Athens Medical School, National and Kapodistrian University of Athens, Athens, Greece
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  givenname: Antoine
  orcidid: 0000-0001-7133-1788
  surname: Froidure
  fullname: Froidure, Antoine
  organization: Cliniques Universitaires Saint-Luc, Service de Pneumologie, Bruxelles, France
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  givenname: Stéphane
  orcidid: 0000-0002-1949-3461
  surname: Jouneau
  fullname: Jouneau, Stéphane
  organization: Center for rare pulmonary disease, Centre Hospitalier Universitaire de Rennes, Service de Pneumologie, - IRSET (Institut de recherche en santé, environnement et travail) - UMR_S 1085, Université de Rennes 1, Rennes, France
– sequence: 13
  givenname: Lidwine
  surname: Wemeau
  fullname: Wemeau, Lidwine
  organization: Reference center for rare pulmonary diseases, Service de Pneumologie, CHRU de Lille, Lille, France
– sequence: 14
  givenname: Claire
  surname: Andrejak
  fullname: Andrejak, Claire
  organization: Center for rare pulmonary disease, Service de Pneumologie, Hôpital d'Amiens, Université de Picardie Jules Verne, Amiens, France
– sequence: 15
  givenname: Anne
  surname: Gondouin
  fullname: Gondouin, Anne
  organization: Center for rare pulmonary disease CHU de Besançon, Service de Pneumologie, Besançon, France
– sequence: 16
  givenname: Sandrine
  surname: Hirschi
  fullname: Hirschi, Sandrine
  organization: Center for rare pulmonary disease, Service de Pneumologie, Groupe de Transplantation Pulmonaire, Hôpitaux Universitaires de Strasbourg, Strasbourg, France
– sequence: 17
  givenname: Elodie
  surname: Blanchard
  fullname: Blanchard, Elodie
  organization: Center for rare pulmonary disease, CHU de Bordeaux, Service de Pneumologie, Pessac, France
– sequence: 18
  givenname: Benjamin
  surname: Bondue
  fullname: Bondue, Benjamin
  organization: Hôpital Erasme - ULB, Brussels, Belgium
– sequence: 19
  givenname: Philippe
  surname: Bonniaud
  fullname: Bonniaud, Philippe
  organization: Reference center for rare pulmonary diseases, Service de Pneumologie, Dijon, France
– sequence: 20
  givenname: Cécile
  surname: Tromeur
  fullname: Tromeur, Cécile
  organization: CHU de la Cavale Blanche, Département de médecine interne et de pneumologie, Brest, France
– sequence: 21
  givenname: Grégoire
  surname: Prévot
  fullname: Prévot, Grégoire
  organization: Center for rare pulmonary diseases, Service de Pneumologie, Hôpital Larrey, Toulouse, France
– sequence: 22
  givenname: Sylvain
  surname: Marchand-Adam
  fullname: Marchand-Adam, Sylvain
  organization: Center for rare pulmonary diseases, CHU de Tours, Service de Pneumologie et Explorations Fonctionnelles Respiratoires, Tours, France
– sequence: 23
  givenname: Manuela
  surname: Funke-Chambour
  fullname: Funke-Chambour, Manuela
  organization: Service universitaire de pneumologie, Bern, Switzerland
– sequence: 24
  givenname: Anne Sophie
  surname: Gamez
  fullname: Gamez, Anne Sophie
  organization: Center for rare pulmonary diseases, Département de Pneumologie et Addictologie, Hôpital Arnaud de Villeneuve, CHU Montpellier, Montpellier, France
– sequence: 25
  givenname: Ibrahima
  surname: Ba
  fullname: Ba, Ibrahima
  organization: Dept of Genetics, APHP, Hôpital Bichat, Paris, France
– sequence: 26
  givenname: Spyridon
  surname: Papiris
  fullname: Papiris, Spyridon
  organization: Respiratory Medicine Dept, 'Attikon' University Hospital, Athens Medical School, National and Kapodistrian University of Athens, Athens, Greece
– sequence: 27
  givenname: Jan
  surname: Grutters
  fullname: Grutters, Jan
  organization: Interstitial Lung Diseases Center of Excellence, Dept of Pulmonology, St Antonius Hospital, Nieuwegein, The Netherlands
– sequence: 28
  givenname: Bruno
  surname: Crestani
  fullname: Crestani, Bruno
  organization: OrphaLung Network, Paris, France
– sequence: 29
  givenname: Coline
  surname: van Moorsel
  fullname: van Moorsel, Coline
  organization: Interstitial Lung Diseases Center of Excellence, Dept of Pulmonology, St Antonius Hospital, Nieuwegein, The Netherlands
– sequence: 30
  givenname: Caroline
  orcidid: 0000-0003-2155-9383
  surname: Kannengiesser
  fullname: Kannengiesser, Caroline
  organization: Dept of Genetics, APHP, Hôpital Bichat, Paris, France
– sequence: 31
  givenname: Raphaël
  orcidid: 0000-0002-9906-0024
  surname: Borie
  fullname: Borie, Raphaël
  organization: OrphaLung Network, Paris, France
BackLink https://www.ncbi.nlm.nih.gov/pubmed/33214205$$D View this record in MEDLINE/PubMed
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Title Safety and efficacy of pirfenidone and nintedanib in patients with idiopathic pulmonary fibrosis and carrying a telomere-related gene mutation
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