Výsledky vyhľadávania - "fibrosis"
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1
Autori: a ďalší
Zdroj: Molecular therapy : the journal of the American Society of Gene Therapy [Mol Ther] 2025 Dec 03; Vol. 33 (12), pp. 6463-6478. Date of Electronic Publication: 2025 Sep 08.
Spôsob vydávania: Journal Article
Informácie o časopise: Publisher: Cell Press Country of Publication: United States NLM ID: 100890581 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1525-0024 (Electronic) Linking ISSN: 15250016 NLM ISO Abbreviation: Mol Ther Subsets: MEDLINE
Výrazy zo slovníka MeSH: Cystic Fibrosis*/metabolism , Cystic Fibrosis*/genetics , Cystic Fibrosis*/therapy , Anoctamin-1*/genetics , Anoctamin-1*/metabolism , Oligonucleotides, Antisense*/genetics , Oligonucleotides, Antisense*/pharmacology , Oligonucleotides, Antisense*/administration & dosage , Chlorides*/metabolism , Neoplasm Proteins*/genetics , Neoplasm Proteins*/metabolism, Animals ; Mice ; Humans ; Cystic Fibrosis Transmembrane Conductance Regulator/genetics ; Cystic Fibrosis Transmembrane Conductance Regulator/metabolism ; Disease Models, Animal
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2
Autori: a ďalší
Zdroj: Cell biology international [Cell Biol Int] 2025 Dec; Vol. 49 (12), pp. 1564-1578. Date of Electronic Publication: 2025 Sep 22.
Spôsob vydávania: Journal Article; Review
Informácie o časopise: Publisher: Chichester Country of Publication: England NLM ID: 9307129 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1095-8355 (Electronic) Linking ISSN: 10656995 NLM ISO Abbreviation: Cell Biol Int Subsets: MEDLINE
Výrazy zo slovníka MeSH: Cystic Fibrosis*/genetics , Cystic Fibrosis*/therapy , Cystic Fibrosis*/diagnosis , Gene Editing*/methods , CRISPR-Cas Systems*/genetics , Genetic Therapy*/methods, Humans ; Cystic Fibrosis Transmembrane Conductance Regulator/genetics ; Cystic Fibrosis Transmembrane Conductance Regulator/metabolism ; Mutation/genetics ; Animals
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3
Autori: a ďalší
Korporácia: a ďalší
Zdroj: Annals of the American Thoracic Society [Ann Am Thorac Soc] 2025 Nov; Vol. 22 (11), pp. 1696-1708.
Spôsob vydávania: Journal Article; Observational Study; Multicenter Study
Informácie o časopise: Publisher: American Thoracic Society Country of Publication: United States NLM ID: 101600811 Publication Model: Print Cited Medium: Internet ISSN: 2325-6621 (Electronic) Linking ISSN: 23256621 NLM ISO Abbreviation: Ann Am Thorac Soc Subsets: MEDLINE
Výrazy zo slovníka MeSH: Aminophenols*/therapeutic use , Benzodioxoles*/therapeutic use , Cystic Fibrosis*/drug therapy , Cystic Fibrosis*/physiopathology , Indoles*/therapeutic use , Pyrazoles*/therapeutic use , Pyridines*/therapeutic use , Quinolones*/therapeutic use, Child ; Female ; Humans ; Male ; Chloride Channel Agonists/therapeutic use ; Cystic Fibrosis Transmembrane Conductance Regulator ; Drug Combinations ; Forced Expiratory Volume ; Prospective Studies ; Sputum/microbiology ; Sweat/chemistry ; Treatment Outcome ; Quinolines
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4
Autori: a ďalší
Zdroj: Respiratory investigation [Respir Investig] 2025 Nov; Vol. 63 (6), pp. 1132-1138. Date of Electronic Publication: 2025 Sep 19.
Spôsob vydávania: Journal Article
Informácie o časopise: Publisher: Elsevier Country of Publication: Netherlands NLM ID: 101581124 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 2212-5353 (Electronic) Linking ISSN: 22125345 NLM ISO Abbreviation: Respir Investig Subsets: MEDLINE
Výrazy zo slovníka MeSH: Lung Transplantation* , Pulmonary Fibrosis*/mortality , Pulmonary Fibrosis*/surgery , Pulmonary Fibrosis*/physiopathology, Humans ; Retrospective Studies ; Prognosis ; Male ; Female ; Waiting Lists/mortality ; Middle Aged ; Disease Progression ; Aged ; Idiopathic Pulmonary Fibrosis/mortality ; Idiopathic Pulmonary Fibrosis/surgery ; Vital Capacity ; Lung Diseases, Interstitial/surgery ; Lung Diseases, Interstitial/mortality
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5
Autori: a ďalší
Zdroj: Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society [J Cyst Fibros] 2025 Nov; Vol. 24 (6), pp. 1156-1165. Date of Electronic Publication: 2025 Aug 15.
Spôsob vydávania: Journal Article
Informácie o časopise: Publisher: Elsevier Country of Publication: Netherlands NLM ID: 101128966 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1873-5010 (Electronic) Linking ISSN: 15691993 NLM ISO Abbreviation: J Cyst Fibros Subsets: MEDLINE
Výrazy zo slovníka MeSH: Cystic Fibrosis*/genetics , Cystic Fibrosis*/metabolism , Cystic Fibrosis*/pathology , Cystic Fibrosis*/physiopathology , Epithelial Cells*/metabolism , Epithelial Cells*/pathology , Hypoxia*/metabolism , Respiratory Mucosa*/pathology , Respiratory Mucosa*/metabolism, Humans ; Cystic Fibrosis Transmembrane Conductance Regulator/genetics ; Cystic Fibrosis Transmembrane Conductance Regulator/metabolism ; Hypoxia-Inducible Factor 1, alpha Subunit/metabolism ; Hypoxia-Inducible Factor 1, alpha Subunit/genetics ; Cell Hypoxia ; Signal Transduction
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6
Autori: a ďalší
Zdroj: International journal of molecular sciences [Int J Mol Sci] 2025 Oct 10; Vol. 26 (20). Date of Electronic Publication: 2025 Oct 10.
Spôsob vydávania: Journal Article; Review
Informácie o časopise: Publisher: MDPI Country of Publication: Switzerland NLM ID: 101092791 Publication Model: Electronic Cited Medium: Internet ISSN: 1422-0067 (Electronic) Linking ISSN: 14220067 NLM ISO Abbreviation: Int J Mol Sci Subsets: MEDLINE
Výrazy zo slovníka MeSH: Cystic Fibrosis*/drug therapy , Cystic Fibrosis*/metabolism , Receptors, Aryl Hydrocarbon*/metabolism , Indoles*/therapeutic use , Indoles*/pharmacology, Humans ; Cystic Fibrosis Transmembrane Conductance Regulator/metabolism ; Cystic Fibrosis Transmembrane Conductance Regulator/genetics ; Signal Transduction/drug effects ; Animals
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7
Autori: a ďalší
Zdroj: Pediatric pulmonology [Pediatr Pulmonol] 2025 Dec; Vol. 60 (12), pp. e71419.
Spôsob vydávania: Journal Article; Comparative Study
Informácie o časopise: Publisher: Wiley-Liss Country of Publication: United States NLM ID: 8510590 Publication Model: Print Cited Medium: Internet ISSN: 1099-0496 (Electronic) Linking ISSN: 10990496 NLM ISO Abbreviation: Pediatr Pulmonol Subsets: MEDLINE
Výrazy zo slovníka MeSH: Cystic Fibrosis*/complications , Cystic Fibrosis*/physiopathology , Olfaction Disorders*/etiology , Olfaction Disorders*/physiopathology , Taste Disorders*/etiology , Taste Disorders*/physiopathology , Ciliary Motility Disorders*/complications , Ciliary Motility Disorders*/physiopathology, Humans ; Prospective Studies ; Male ; Female ; Child ; Adolescent ; Young Adult ; Adult ; Case-Control Studies ; Iontophoresis ; Cystic Fibrosis Transmembrane Conductance Regulator/genetics ; Spirometry
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8
Autori: a ďalší
Korporácia: a ďalší
Zdroj: Clinical microbiology and infection : the official publication of the European Society of Clinical Microbiology and Infectious Diseases [Clin Microbiol Infect] 2025 Dec; Vol. 31 (12), pp. 2011-2017. Date of Electronic Publication: 2025 Aug 20.
Spôsob vydávania: Journal Article; Observational Study
Informácie o časopise: Publisher: Elsevier Country of Publication: England NLM ID: 9516420 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1469-0691 (Electronic) Linking ISSN: 1198743X NLM ISO Abbreviation: Clin Microbiol Infect Subsets: MEDLINE
Výrazy zo slovníka MeSH: Cystic Fibrosis*/drug therapy , Cystic Fibrosis*/microbiology , Cystic Fibrosis*/complications , Aminophenols*/therapeutic use , Quinolones*/therapeutic use , Benzodioxoles*/therapeutic use , Pyridines*/therapeutic use , Indoles*/therapeutic use , Pyrazoles*/therapeutic use , Respiratory Tract Infections*/microbiology , Respiratory Tract Infections*/epidemiology , Lung*/microbiology, Humans ; Male ; Female ; Denmark/epidemiology ; Adolescent ; Child ; Drug Combinations ; Sputum/microbiology ; Young Adult ; Adult ; Cohort Studies ; Cystic Fibrosis Transmembrane Conductance Regulator/genetics ; Bacteria/isolation & purification ; Quinolines
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9
Autori: a ďalší
Zdroj: Pediatric nephrology (Berlin, Germany) [Pediatr Nephrol] 2025 Dec; Vol. 40 (12), pp. 3605-3614. Date of Electronic Publication: 2025 Mar 17.
Spôsob vydávania: Journal Article; Review
Informácie o časopise: Publisher: Springer International Country of Publication: Germany NLM ID: 8708728 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1432-198X (Electronic) Linking ISSN: 0931041X NLM ISO Abbreviation: Pediatr Nephrol Subsets: MEDLINE
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10
Autori: a ďalší
Zdroj: Pathogens (Basel, Switzerland) [Pathogens] 2025 Nov 12; Vol. 14 (11). Date of Electronic Publication: 2025 Nov 12.
Spôsob vydávania: Journal Article
Informácie o časopise: Publisher: MDPI AG Country of Publication: Switzerland NLM ID: 101596317 Publication Model: Electronic Cited Medium: Internet ISSN: 2076-0817 (Electronic) Linking ISSN: 20760817 NLM ISO Abbreviation: Pathogens Subsets: MEDLINE
Výrazy zo slovníka MeSH: Cystic Fibrosis*/microbiology , Cystic Fibrosis*/genetics , Cystic Fibrosis*/metabolism , Cystic Fibrosis*/pathology , Pseudomonas aeruginosa*/pathogenicity , Sphingosine-1-Phosphate Receptors*/metabolism , Sphingosine-1-Phosphate Receptors*/genetics , Pseudomonas Infections*/microbiology , Pseudomonas Infections*/metabolism , Pseudomonas Infections*/genetics , Pseudomonas Infections*/pathology , Epithelial Cells*/microbiology , Epithelial Cells*/metabolism , Respiratory Mucosa*/microbiology , Respiratory Mucosa*/metabolism, Humans ; Cystic Fibrosis Transmembrane Conductance Regulator/genetics ; Interleukin-8/metabolism ; Cell Line ; Cell Survival
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11
Autori: a ďalší
Zdroj: Pediatric pulmonology [Pediatr Pulmonol] 2025 Nov; Vol. 60 (11), pp. e71386.
Spôsob vydávania: Journal Article
Informácie o časopise: Publisher: Wiley-Liss Country of Publication: United States NLM ID: 8510590 Publication Model: Print Cited Medium: Internet ISSN: 1099-0496 (Electronic) Linking ISSN: 10990496 NLM ISO Abbreviation: Pediatr Pulmonol Subsets: MEDLINE
Výrazy zo slovníka MeSH: Cystic Fibrosis*/diagnosis , Cystic Fibrosis*/genetics , Neonatal Screening*/methods , Genetic Testing*/methods, Humans ; Canada/epidemiology ; Infant, Newborn ; Cystic Fibrosis Transmembrane Conductance Regulator/genetics ; Registries ; Trypsinogen/blood
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12
Autori: a ďalší
Zdroj: Respiratory medicine and research [Respir Med Res] 2025 Nov; Vol. 88, pp. 101186. Date of Electronic Publication: 2025 Jun 16.
Spôsob vydávania: Journal Article; Observational Study
Informácie o časopise: Publisher: Elsevier Masson SAS Country of Publication: France NLM ID: 101746324 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 2590-0412 (Electronic) Linking ISSN: 25900412 NLM ISO Abbreviation: Respir Med Res Subsets: MEDLINE
Výrazy zo slovníka MeSH: Cystic Fibrosis*/therapy , Cystic Fibrosis*/drug therapy , Self Medication*/statistics & numerical data , Complementary Therapies*/statistics & numerical data , Complementary Therapies*/methods, Humans ; Male ; Adult ; Female ; Child ; Adolescent ; Young Adult ; Middle Aged ; France/epidemiology ; Drug Interactions ; Cystic Fibrosis Transmembrane Conductance Regulator ; Surveys and Questionnaires ; Child, Preschool
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13
Autori: a ďalší
Zdroj: Biomedicine & pharmacotherapy = Biomedecine & pharmacotherapie [Biomed Pharmacother] 2025 Nov; Vol. 192, pp. 118558. Date of Electronic Publication: 2025 Sep 18.
Spôsob vydávania: Journal Article
Informácie o časopise: Publisher: Editions Scientifiques Elsevier Country of Publication: France NLM ID: 8213295 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1950-6007 (Electronic) Linking ISSN: 07533322 NLM ISO Abbreviation: Biomed Pharmacother Subsets: MEDLINE
Výrazy zo slovníka MeSH: Cystic Fibrosis*/drug therapy , Cystic Fibrosis*/metabolism , Cystic Fibrosis*/blood , Aminophenols*/analysis , Aminophenols*/pharmacokinetics , Aminophenols*/blood , Aminophenols*/therapeutic use , Drug Monitoring*/methods , Quinolones*/analysis , Quinolones*/pharmacokinetics , Quinolones*/blood , Quinolones*/therapeutic use , Benzodioxoles*/analysis , Benzodioxoles*/pharmacokinetics , Benzodioxoles*/blood , Benzodioxoles*/therapeutic use , Sweat*/chemistry , Sweat*/metabolism , Tandem Mass Spectrometry*/methods , Indoles*/analysis , Indoles*/pharmacokinetics , Indoles*/blood , Pyrazoles*/analysis , Pyrazoles*/pharmacokinetics , Pyrazoles*/blood , Pyridines*/analysis , Pyridines*/pharmacokinetics , Pyridines*/blood , Chloride Channel Agonists*/analysis , Chloride Channel Agonists*/pharmacokinetics , Pyrrolidines*/analysis, Humans ; Drug Combinations ; Cystic Fibrosis Transmembrane Conductance Regulator/metabolism ; Chromatography, Liquid/methods ; Dried Blood Spot Testing/methods ; Reproducibility of Results ; Liquid Chromatography-Mass Spectrometry ; Quinolines
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14
Autori: a ďalší
Zdroj: Respiratory medicine [Respir Med] 2025 Nov-Dec; Vol. 249, pp. 108393. Date of Electronic Publication: 2025 Oct 17.
Spôsob vydávania: Journal Article; Observational Study
Informácie o časopise: Publisher: Elsevier Country of Publication: England NLM ID: 8908438 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1532-3064 (Electronic) Linking ISSN: 09546111 NLM ISO Abbreviation: Respir Med Subsets: MEDLINE
Výrazy zo slovníka MeSH: Cystic Fibrosis*/epidemiology , Cystic Fibrosis*/genetics , Cystic Fibrosis*/physiopathology, Humans ; Male ; Female ; Egypt/epidemiology ; Child ; Registries ; Child, Preschool ; Cystic Fibrosis Transmembrane Conductance Regulator/genetics ; Adolescent ; Mutation ; Severity of Illness Index ; Genotype ; Infant
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15
Autori:
Zdroj: Current opinion in pulmonary medicine [Curr Opin Pulm Med] 2025 Nov 01; Vol. 31 (6), pp. 644-649. Date of Electronic Publication: 2025 Sep 03.
Spôsob vydávania: Journal Article; Review
Informácie o časopise: Publisher: Lippincott Williams & Wilkins Country of Publication: United States NLM ID: 9503765 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1531-6971 (Electronic) Linking ISSN: 10705287 NLM ISO Abbreviation: Curr Opin Pulm Med Subsets: MEDLINE
Výrazy zo slovníka MeSH: Cystic Fibrosis*/therapy , Cystic Fibrosis*/drug therapy , COVID-19*/epidemiology, Humans ; Telemedicine ; SARS-CoV-2 ; Cystic Fibrosis Transmembrane Conductance Regulator ; Disease Progression
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16
Autori: a ďalší
Zdroj: Chembiochem : a European journal of chemical biology [Chembiochem] 2025 Oct 31; Vol. 26 (20), pp. e202500586. Date of Electronic Publication: 2025 Oct 10.
Spôsob vydávania: Journal Article; Review
Informácie o časopise: Publisher: Wiley-VCH Verlag Country of Publication: Germany NLM ID: 100937360 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1439-7633 (Electronic) Linking ISSN: 14394227 NLM ISO Abbreviation: Chembiochem Subsets: MEDLINE
Výrazy zo slovníka MeSH: Cystic Fibrosis*/drug therapy , Cystic Fibrosis*/metabolism , Flavonoids*/therapeutic use , Flavonoids*/chemistry , Flavonoids*/pharmacology , Citrus*/chemistry, Humans ; Cystic Fibrosis Transmembrane Conductance Regulator/metabolism ; Anti-Inflammatory Agents/chemistry ; Anti-Inflammatory Agents/pharmacology ; Anti-Inflammatory Agents/therapeutic use ; Anti-Bacterial Agents/chemistry ; Anti-Bacterial Agents/pharmacology ; Anti-Bacterial Agents/therapeutic use ; Animals
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17
Autori: a ďalší
Korporácia: a ďalší
Zdroj: International journal of molecular sciences [Int J Mol Sci] 2025 Oct 29; Vol. 26 (21). Date of Electronic Publication: 2025 Oct 29.
Spôsob vydávania: Journal Article; Multicenter Study; Observational Study
Informácie o časopise: Publisher: MDPI Country of Publication: Switzerland NLM ID: 101092791 Publication Model: Electronic Cited Medium: Internet ISSN: 1422-0067 (Electronic) Linking ISSN: 14220067 NLM ISO Abbreviation: Int J Mol Sci Subsets: MEDLINE
Výrazy zo slovníka MeSH: Aminophenols*/therapeutic use , Aminophenols*/adverse effects , Benzodioxoles*/therapeutic use , Benzodioxoles*/adverse effects , Cystic Fibrosis*/drug therapy , Cystic Fibrosis*/genetics , Indoles*/therapeutic use , Indoles*/adverse effects , Pyrazoles*/therapeutic use , Pyrazoles*/adverse effects , Pyridines*/therapeutic use , Pyridines*/adverse effects , Quinolines*/adverse effects , Quinolines*/therapeutic use, Adolescent ; Adult ; Child ; Female ; Humans ; Male ; Middle Aged ; Young Adult ; Cystic Fibrosis Transmembrane Conductance Regulator/genetics ; Drug Combinations ; Retrospective Studies ; Treatment Outcome
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18
Autori: a ďalší
Zdroj: Stem cell research & therapy [Stem Cell Res Ther] 2025 Oct 21; Vol. 16 (1), pp. 573. Date of Electronic Publication: 2025 Oct 21.
Spôsob vydávania: Journal Article
Informácie o časopise: Publisher: BioMed Central Country of Publication: England NLM ID: 101527581 Publication Model: Electronic Cited Medium: Internet ISSN: 1757-6512 (Electronic) Linking ISSN: 17576512 NLM ISO Abbreviation: Stem Cell Res Ther Subsets: MEDLINE
Výrazy zo slovníka MeSH: Induced Pluripotent Stem Cells*/metabolism , Induced Pluripotent Stem Cells*/cytology , Cystic Fibrosis*/pathology , Cystic Fibrosis*/metabolism , Cystic Fibrosis*/genetics , Mucociliary Clearance*, Humans ; Cystic Fibrosis Transmembrane Conductance Regulator/metabolism ; Cystic Fibrosis Transmembrane Conductance Regulator/genetics ; Cell Differentiation ; Cells, Cultured ; Cilia/metabolism
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19
Autori: a ďalší
Zdroj: Human mutation [Hum Mutat] 2025 Oct 19; Vol. 2025, pp. 7570437. Date of Electronic Publication: 2025 Oct 19 (Print Publication: 2025).
Spôsob vydávania: Journal Article
Informácie o časopise: Publisher: Wiley-Liss Country of Publication: United States NLM ID: 9215429 Publication Model: eCollection Cited Medium: Internet ISSN: 1098-1004 (Electronic) Linking ISSN: 10597794 NLM ISO Abbreviation: Hum Mutat Subsets: MEDLINE
Výrazy zo slovníka MeSH: Cystic Fibrosis*/genetics , Cystic Fibrosis*/complications , Pain*/genetics , Pain*/etiology , Genes, Modifier*, Humans ; Computational Biology/methods ; Computer Simulation ; Cystic Fibrosis Transmembrane Conductance Regulator/genetics ; Phenotype ; Protein Interaction Maps ; Gene Regulatory Networks ; Genetic Association Studies ; Genetic Predisposition to Disease
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20
Autori: a ďalší
Zdroj: Cell biology international [Cell Biol Int] 2025 Oct; Vol. 49 (10), pp. 1245-1261. Date of Electronic Publication: 2025 Jul 01.
Spôsob vydávania: Journal Article
Informácie o časopise: Publisher: Chichester Country of Publication: England NLM ID: 9307129 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1095-8355 (Electronic) Linking ISSN: 10656995 NLM ISO Abbreviation: Cell Biol Int Subsets: MEDLINE
Výrazy zo slovníka MeSH: Proto-Oncogene Proteins c-akt*/metabolism , Phosphatidylinositol 3-Kinases*/metabolism , Pulmonary Fibrosis*/metabolism , Pulmonary Fibrosis*/pathology, Animals ; Mice ; Signal Transduction ; Humans ; Cell Proliferation ; Male ; Mice, Inbred C57BL ; Cell Line ; Cell Movement ; Disease Models, Animal ; Transforming Growth Factor beta1/metabolism ; Disease Progression ; Idiopathic Pulmonary Fibrosis/metabolism
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